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권순효 ( Soon Hyo Kwon ),나선재 ( Sun Jae Na ),염꽃보라 ( Kkot Bora Yeom ),허선영 ( Sun Young Huh ),나정임 ( Jung Im Na ) 대한피부과학회 2011 대한피부과학회지 Vol.49 No.8
Multiple congenital melanocytic nevi (MCMN), defined as the distribution of more than three small- or medium-sized congenital melanocytic nevi (CMN) on the body without a giant CMN, is a rare disease comprising about 4% of patients with CMN. Because MCMN accompanies neurodevelopmental delay, including seizures in 25% of patients as well as the risk of malignant melanoma, it must be carefully followed-up. We report a case of MCMN with developmental delay in a 19-month-old Korean boy. He had a history of febrile seizure when he was 18 months old. He showed a speech delay after the 1-year-follow up, even though there was no evidence of neurocutaneous melanosis (NCM) on brain magnetic resonance imaging (MRI) at the first visit. As MRI has a low sensitivity for detecting NCM in patients with MCMN older than 4-months, close neurodevelopmental assessments should be considered to provide a chance for early rehabilitation. (Korean J Dermatol 2011;49(8):753∼756)