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( You-sub Kim ),( Kyung-sub Moon ),( Gun-woo Kim ),( Sang Chul Lim ),( Kyung-hwa Lee ),( Woo-youl Jang ),( Tae-young Jung ),( In-young Kim ),( Shin Jung ) 대한뇌종양학회·대한신경종양학회·대한소아뇌종양학회 2015 Brain Tumor Research and Treatment Vol.3 No.2
Background Craniofacial resection (CFR) has been regarded as a standard treatment for various tumors involving the anterior skull base. The purpose of this study was to evaluate the results of CFR for the patients with anterior skull base malignancies in our hospital. Methods We retrospectively analyzed 17 patients with anterior skull base malignancies treated with CFR between 2001 and 2012. Mean follow-up duration was 41 months (range, 2-103 months). Results Intracranial involvement was found in 11 patients (65%) and orbital extension in 6 patients (35%). Classical bifrontal craniotomy was combined with endoscopic endonasal approach in 14 patients and external approach in 3 patients. Vascularized flap was used for reconstruction of the anterior fossa floor in 16 patients (94%). The most common pathological type was squamous cell carcinoma (6 patients). Gross total resection was achieved in all cases. Postoperative complications developed in 4 patients (24%) and included local wound problem and brain abscess. One patient with liver cirrhosis died from unexpected varix bleeding after the operation. Although postoperative treatment, such as radiotherapy or chemotherapy, was performed in 14 patients, local recurrence was seen in 6 patients. The mean overall survival time after the operation was 69.0 months (95% confidence interval: 47.5-90.5 months) with a 1-, 2-, and 5-year survival rate of 82.3%, 76.5%, and 64.7%, respectively. Postoperative radiotherapy was found to be the powerful prognostic factor for favorable survival. Conclusion Considering the higher local control rate and acceptable complication or mortality rate, CFR with adjuvant radiotherapy is a gold standard treatment option for malignant tumors involving anterior skull base, especially with extensive intracranial involvement.
광범위한 뇌연수막 파종으로 나타난 역형성 성상세포종의 특이 발현 Temozolomide를 기초로 치료한 두 증례 보고
최정원 ( Jung Won Choi ),김인아 ( In A Kim ),최기영 ( Ghee Young Choe ),김재용 ( Chae Yong Kim ) 대한뇌종양학회·대한신경종양학회·대한소아뇌종양학회 2008 대한뇌종양학회지 Vol.7 No.2
We describe two unusual cases of diffuse leptomeningeal seeding as the initial manifestation of a subtle brain mass lesion. At first, they were misdiagnosed as tuberculous encephalitis because there was no obvious mass lesion in magnetic resonance(MR) images of the brain and the cerebrospinal fluid profile was highly suggestive of an infective process. The MR images showed only ill-defined lesions in the basal ganglia. Anaplastic astrocytomas were finally diagnosed following stereotactic brain biopsies. Whole-spine MR images from these two patients revealed diffuse leptomeningeal enhancing lesions that affected the whole spine. We planned aggressive multimodal treatment including concurrent chemoradiation therapy using temozolomide. One patient died from disease progression eight months after the initial diagnosis. The second patient was treated more aggressively. She survived for more than thirteen months after diagnosis. Biopsy and aggressive treatment must be considered in cases of ill-defined lesions with clinical manifestation indicating unusual encephalitis.
전이성 뇌종양으로 오인된 소뇌의 표피양 낭종 -증례보고-
박원형 ( Won Hyoung Park ),조영현 ( Young Hyun Cho ),김정훈 ( Jeong Hoon Kim ) 대한뇌종양학회·대한신경종양학회·대한소아뇌종양학회 2009 대한뇌종양학회지 Vol.8 No.2
Epidermoid cysts are benign lesions that may arise in the spine or intracranium. And in adult, metastatic brain tumors are the most common intracranial neoplasm. But, the treatment and prognosis are very different between epidermoid cysts and metastatic brain tumors. We report one case of patient who had cerebellar epidermoid cyst mimicking brain metastasis.
( Tae Yong Park ),( Young Chul Na ),( Won Hee Lee ),( Ji Hee Kim ),( Won Seok Chang ),( Hyun Ho Jung ),( Jong Hee Chang ),( Jin Woo Chang ),( Young Gou Park ) 대한뇌종양학회·대한신경종양학회·대한소아뇌종양학회 2013 Brain Tumor Research and Treatment Vol.1 No.2
Objective: Although metastasis of hepatocellular carcinoma to the brain is uncommon, it is associated with a very high mortality rate and most patients usually expire within 1 year after brain metastasis. The aim of this study is to identify the effectiveness of the active interventions such as gamma knife radiosurgery or surgical intervention for these patients. Methods: We retrospectively reviewed the medical records and imaging data of 59 patients with metastatic brain tumors from hepatocellular carcinoma from May 2004 to September 2012. The study included patients with available clinical and radiological data who had been diagnosed with metastatic hepatocellular carcinoma of the brain, confirmed by magnetic resonance imaging. The overall survival time was analyzed and compared according to each risk factor. Results: The mean age at diagnosis of metastatic brain tumor was 52.2 years (14-77). The mean follow-up duration was 13.3 weeks (0.1-117.6). Overall median survival was 4.3 weeks (95% confidence interval, 2.2-6.4). The results from an analysis of clinical factors related to survival revealed that treatment modalities were significantly related to the patient`s survival (log rank, p=0.006). Twenty patients (32.8%) experienced tumor bleeding, and the survival time of the patients with tumor bleeding tended to be shorter, although the result was not statistically significant (log rank, p=0.058). Hepatic reserve, by Child-Pugh classification, was grade A in 38 patients (64.4%), grade B in 16 patients (27.1%), and grade C in 5 patients (8.5%), and was significantly related to the patient`s survival (log rank, p=0.000). Conclusion: Although patients with metastatic brain tumors from hepatocellular carcinoma showed poor survival, active intervention including surgical resection or gamma knife radiosurgery may result in better survival, especially if patients have preserved liver function.
측뇌실 삼각에 발생한 뇌실내 수막종에 있어 상부 두정-후두 피질경유 접근법의 임상 결과 ; 24례 보고
박세환 ( Se Hwan Park ),조진모 ( Jin Mo Cho ),김의현 ( Eui Hyun Kim ),김선호 ( Sun Ho Kim ),이규성 ( Kyu Sung Lee ),장종희 ( Jong Hee Chang ) 대한뇌종양학회·대한신경종양학회·대한소아뇌종양학회 2012 대한뇌종양학회지 Vol.11 No.2
Introduction:Intraventricular meningiomas are uncommon subtype of intracranial meningiomas. Trigonal meningiomas consist of the majority of intraventricular meningiomas. The superior parieto-occipital transcortical approach is the most popular approach for removal of them. We analyzed our experience in removal of the trigonal meningiomas that were resected using the superior parieto-occipital transcortical approach. Patients and Methods:Twenty-four patients underwent surgical removal of trigonal meningioma from 1997 to May 2012. Demographics, clinical features, surgical outcomes, histopathologic results and prognosis were analyzed. Results:Study population had a mean age of 51.2 years and a female preponderance of 1 : 1.7. The most common presenting symptom was chronic headache, which was followed by memory impairment, visual disturbance and hemiparesis. Total removal of the tumor was achieved in all cases. Twenty-two (91.7%) tumors were World Health Organization (WHO) grade I while two cases were WHO grade III. There were two cases of intracerebral hemorrhage in the surgical corridor, one case of transient contralateral hemiparesis with cognitive decline, one case of transient contralateral homonymous hemianopsia, one case of aggravation of visual field defect, and one case of hydrocephalus which was successfully treated by ventriculo-peritoneal shunt. Conclusion:The superior parieto-occipital approach is suitable for most of the trigonal meningiomas and total removal of them can be achieved safely.
김성진 ( Sung Jin Kim ),한성록 ( Seong Rok Han ),윤상원 ( Sang Won Yoon ),이기택 ( Gi Taek Yee ),최찬영 ( Chan Young Choi ),손문준 ( Moon Jun Sohn ),이동준 ( Dong Joon Lee ),김한성 ( Han Seong Kim ),황충진 ( Choong Jin Whang ) 대한뇌종양학회·대한신경종양학회·대한소아뇌종양학회 2006 대한뇌종양학회지 Vol.5 No.2
Despite multimodal therapy, glioblastoma multiforme(GBM) is associated with a poor prognosis with a median survival of less than 1 year. GBM with long-term survival over 5 years is rare, and no definite markers of better prognosis have been identified till date. We present two patients who were diagnosed a frontal GBM and a cerebellar GBM respectively. Both patients were survived for more than 5 years, who had been treated with surgery, Novalis radiosurgery and chemotherapy. We also discussed prognostic factors who were long term survival with GBM.
( Sarah Nicholas ),( Dimitris Mathios ),( Jacob Ruzevick ),( Christopher Jackson ),( Isaac Yang ),( Michael Lim ) 대한뇌종양학회·대한신경종양학회·대한소아뇌종양학회 2013 Brain Tumor Research and Treatment Vol.1 No.1
Glioblastoma multiforme (GBM) is the most common primary brain cancer. Even with aggressive combination therapy, the median life expectancy for patients with GBM remains approximately 14 months. In order to improve the outcomes of patients with GBM, the development of newer treatments is critical. The concept of using the immune system as a therapeutic option has been suggested for several decades; by harnessing the body`s adaptive immune mechanisms, immunotherapy could provide a durable and targeted treatment against cancer. However, many cancers, including GBM, have developed mechanisms that protect tumor cells from being recognized and eliminated by the immune system. For new immunotherapeutic regimens to be successful, overcoming immunosuppression via immune checkpoint signaling should be taken into consideration.
Cowden병과 동반된 Lhermitte-Duclos병 -증례보고-
이도성 ( Do Sung Lee ),김대원 ( Dae Won Kim ),김태영 ( Tae Young Kim ),김종문 ( Jong Moon Kim ) 대한뇌종양학회·대한신경종양학회·대한소아뇌종양학회 2005 대한뇌종양학회지 Vol.4 No.2
Lhermitte-Duclos disease(LDD), or dysplastic gangliocytoma is a benign hamartoma arising from cerebellar cortex. Cowden disease(CD) is a rare autosomal dominant disease that usually presents with multiple mucocutaneous lesions and a significant number of patients with CD develop systemic malignancies. Recent studies have demonstrated that Lhermitte- Duclos disease is a part of Cowden disease, a new phakomatosis. The authors report a patient of 27-year-old female with LDD in both cerebellar hemispheres. She had admitted in our department 4 years ago and we misdiagnosed it as a cerebellar infarction in both PICA territories. After systemic evaluation, CD was diagnosed.
Pain Assessment in Brain Tumor Patients after Elective Craniotomy
( Young Deok Kim ),( Jae Hyun Park ),( Seung Ho Yang ),( Il Sup Kim ),( Jae Taek Hong ),( Jae Hoon Sung ),( Byung Chul Son ),( Sang Won Lee ) 대한뇌종양학회·대한신경종양학회·대한소아뇌종양학회 2013 Brain Tumor Research and Treatment Vol.1 No.1
Objective: This study was performed to assess the postoperative pain of brain tumor patients who underwent elective craniotomy and to evaluate the factors associated with pain intensity. Methods: From January 2010 to December 2011, 47 patients with newly diagnosed brain tumors who underwent craniotomy were enrolled. The postoperative pain status was assessed daily until discharge using the visual analogue scale (VAS). Results: The study participants comprised of 22 males and 25 females with ages ranging from 18-76 years (median age, 50 years). Patients were divided into two groups: the painful group included patients who had a VAS score of more than 3 during their hospital stay after the craniotomy, and the tolerable group included patients who had a VAS score of 1 to 3 during their hospital stay. There were no differences between the two groups in terms of age, sex, location of surgery, history of diabetes, hypertension and smoking, body mass index, and hospital stay. Univariate analysis revealed that operating time, length of wound, head fixation, and perioperative administration of opioid were not associated with the intensity of postoperative pain. Daily assessment of VAS revealed the two peaks of pain on the operation day and the 4th postoperative day. The intensity of pain during the ambulation period was higher than that during intensive care unit (ICU) stay. Conclusion: Pain following elective craniotomy for brain tumor removal is insufficiently managed, especially after discharge from the ICU. More attention needs to be paid to patients` pain throughout the hospital stay.
이정훈 ( Jeong Hoon Lee ),공두식 ( Doo Sik Kong ),박관 ( Kwan Park ),김종현 ( Jong Hyun Kim ) 대한뇌종양학회·대한신경종양학회·대한소아뇌종양학회 2008 대한뇌종양학회지 Vol.7 No.2
We report two rare cases of pituitary adenomas arising from the pituitary stalk. The major complaints of both patients were headaches and visual disturbances. On magnetic resonance imaging, both tumors were suprasellar in location. Gross tumor excision was performed via the pterional approach. The pathologic diagnoses were pituitary adenomas in both patients. The tumors were shown to be non-functioning by immunochemistry analyses. No remnant tumors existed postoperatively on follow-up magnetic resonance imaging. The pituitary stalk was preserved in both cases and pituitary hormonal activity remained intact postoperatively. One patient had normal visual function pre- and post-operatively;the other patient had improvement in the visual field defect and temporal hemianopsia involving the left eye. While there are many case reports involving ectopic pituitary adenomas, pituitary adenomas originating from the pituitary stalk are extremely rare.