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Song, K.J.,Ko, R.K.,Kim, H.S.,Ha, H.S.,Ha, D.W.,Oh, S.S.,Park, C.,Yoo, S.-I.,Kim, M.W.,Kim, C.J.,Joo, J.H. Institute of Electrical and Electronics Engineers 2007 IEEE transactions on applied superconductivity Vol.17 No.2
<P>The degree of ferromagnetism of Ni-W<SUB>y</SUB> alloys decreases as W-content y increases. Both the saturation magnetization <I>M</I> <SUB>sat</SUB> and Curie temperature <I>T</I> <SUB>c</SUB> decrease linearly with W-content y, and both <I>M</I> <SUB>sat</SUB> and <I>T</I> <SUB>c</SUB> go to zero at critical concentration of y<SUB>c</SUB> ~9.50 at.% W. To compare with Ni-W alloys, the magnetic properties of a series of both as-rolled (non-textured) and annealed (biaxially textured) [Ni<SUB>97at.%</SUB>-W<SUB>3at.%</SUB>]<SUB>100-x</SUB>-Cu<SUB>x</SUB> alloy tapes with compositions x = 0, 1, 3, 5, and 7 at.%, were studied. Characterization methods included XRD analyses to investigate the biaxial texturing of the annealed [Ni-W]-Cu alloy tapes and studies of the magnetization for both as-rolled and annealed [Ni-W]-Cu alloy tapes. Both the isothermal mass magnetizations <I>M</I>(<I>H</I>) of a series of samples at different fixed temperatures and <I>M</I>(<I>T</I>) in fixed field, were measured. The effect of Cu addition on both the saturation magnetization and Curie temperature T<SUB>c</SUB> of the Ni<SUB>97at.%</SUB>-W<SUB>3at.%</SUB> alloy was investigated.</P>
Novel dentin phosphoprotein frameshift mutations in dentinogenesis imperfecta type II
Lee, K‐,E,Kang, H‐,Y,Lee, S‐,K,Yoo, S‐,H,Lee, J‐,C,Hwang, Y‐,H,Nam, KH,Kim, J‐,S,Park, J‐,C,Kim, J‐,W Blackwell Publishing Ltd 2011 Clinical genetics Vol.79 No.4
<P>Lee K‐E, Kang H‐Y, Lee S‐K, Yoo S‐H, Lee J‐C, Hwang Y‐H, Nam KH, Kim J‐S, Park J‐C, Kim J‐W. Novel dentin phosphoprotein frameshift mutations in dentinogenesis imperfecta type II.</P><P>The dentin sialophosphoprotein (<I>DSPP</I>) gene encodes the most abundant non‐collagenous protein in tooth dentin and DSPP protein is cleaved into several segments including the highly phosphorylated dentin phosphoprotein (DPP). Mutations in the <I>DSPP</I> gene have been solely related to non‐syndromic form of hereditary dentin defects. We recruited three Korean families with dentinogenesis imperfecta (DGI) type II and sequenced the exons and exon–intron boundaries of the <I>DSPP</I> gene based on the candidate gene approach. Direct sequencing of PCR products and allele‐specific cloning of the highly repetitive exon 5 revealed novel single base pair (bp) deletional mutations (c.2688delT and c.3560delG) introducing hydrophobic amino acids in the hydrophilic repeat domain of the DPP coding region. All affected members of the three families showed exceptionally rapid pulp chambers obliteration, even before tooth eruption. Individuals with the c.3560delG mutation showed only mild, yellowish tooth discoloration, in contrast to the affected individuals from two families with c.2688delT mutation. We believe that these results will help us to understand the molecular pathogenesis of DGI type II as well as the normal process of dentin biomineralization.</P>
김종화 ( C H Kim ),이동민 ( D H Lee ),김용성 ( Y S Kim ),최보금 ( B G Choi ),박주형 ( J H Park ),김신재 ( S J Kim ),이치국 ( C K Lee ),전현순 ( H S Jeon ),류완희 ( W H Yoo ),곽재용 ( J Y Kwak ),백홍선 ( H S Baek ) 전북대학교 의과학연구소 2001 全北醫大論文集 Vol.25 No.1
ASU 치료는 증상을 갖고 있는 슬관절의 골관절염 환자의 통증 개선과 관절 기능을 호전시키고, 약물투여 중지 후에 지속효과를 갖는 증상개선 약제로서 안전하게 사용할 수 있을 것으로 보인다. 소염진통제인 naproxen과의 병용치료와의 비교에서는 병용치료 군에서 효과의 발현시기와 전반적인 평가에서는 우월하였으나, 부작용이 보다 많이 발생하였다. 따라서 ASU를 골관절염의 약물치료의 한 방법으로 사용될 수 있을 것으로 보이며, 단순진통제 및 소염진통제 등의 약물 등과 같이 단일요법으로서의 사용과 다른 약물과의 병용치료의 효과 및 안정성에 대해서는 보다 많은 연구가 필요할 것으로 보인다. Objective: To compare the efficacy and safety between avocado/soybean unsaponifiables (ASU) alone and ASU-naproxen combination in the treatment of symptomatic osteoarthritis (OA) of the knee and to determine persistent efficacy after stopping medication and gastrointestinal tolerability. Methods: One hundred twenty-five patients with symptomatic OA of the knee were included in 20-week trial with 12-week treatment period and 8-weeks post-treatment follow-up. Efficacy was evaluated by Lequesne`s index (LI), pain score (VAS; visual analong scale. 10cm) at 4-week interval during the study and physician`s and patient`s global assessment at 20th week. Gastrointestinal side effects were evaluated by questionnaire for gastrointestinal symptoms and number of the ingested antacids during the study. Results: Sixty-three patients were received ASU alone, while sixty-two patients were received ASU and naproxen. Mean±SD scores of pain VAS score were reased from baseline at 8th and 12th weeks after medication in the former groups and 4th, 8th and 12th weeks in the latter groups. Mean±SD scores of LI were decreased from baseline at 12th week after medication in the former groups and 4th, 8th, 12th week in the latter groups. Both scores of LI and pain VAS were maintained at 8th week after stopping medication. The scores of LI and pain VAS scale were significantly decreased in combination group than ASU alone group at 4th and 8th weeks, but tended to lower in combination group at 12th week and post-treatment period. The improvement of physician`s global assessment was seen in 65.4% of combination and 53.2% of ASU alone group. The patient`s global assessment was similar to it. Twenty-six patients (20.8%) could not complete the 20-week study and the causes are different in two groups: side effects are more common cause in combination group and low efficacy and non-compliance were more common in ASU alone group. Gastrointestinal side effects are the most common adverse effects of the both groups, and the frequencies are more common in patients received naproxen as a combination therapy. Conclusion: ASU showed immediate and persistent efficacy in the treatment of patients with symptomatic OA of the knee. The combination of ASU and naproxen was more effective than ASU alone during the treatment period, but similar at post-treatment period. Gastrointestinal side effects were more frequent in combination group than ASU alone.