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Rapidly resolved IgG4-related retroperitoneal fibrosis after steroid pulse therapy
( Soomin Jeung ),( Hyosang Kim ),( Yuri Seo ),( Hee-young Yoon ),( Nah Kyum Lee ),( Shinhee Park ),( Bomi Seo ),( Su-yeon Park ),( Su-kil Park ) 영남대학교 의과대학 2016 Yeungnam University Journal of Medicine Vol.33 No.1
Retroperitoneal fibrosis (RF) is a disorder characterized by the presence of a retroperitoneal mass and concurrent systemic inflammation. Some cases of RF are recognized as belonging to the spectrum of immunoglobulin G4-related disease (IgG4-RD). Glucocorticoids are highly effective for treatment of retroperitoneal fibrosis, although the optimal dose and duration of therapy have not been established. An initial dose of prednisone (40-60 mg) daily is usually administered with a tapering scheme. We report on a 55-year-old man diagnosed with IgG4-related RF and successfully treated with a 3-day course of daily 250 mg (4 mg/kg) intravenous methylprednisolone, which resulted in the prompt resolution of urinary obstruction and systemic symptoms.
Rapidly resolved IgG4-related retroperitoneal fibrosis after steroid pulse therapy
Jeung, Soomin,Kim, Hyosang,Seo, Yuri,Yoon, Hee-Young,Lee, Nah Kyum,Park, Shinhee,Seo, Bomi,Park, Su-Yeon,Park, Su-Kil Yeungnam University College of Medicine 2016 Yeungnam University Journal of Medicine Vol.33 No.1
Retroperitoneal fibrosis (RF) is a disorder characterized by the presence of a retroperitoneal mass and concurrent systemic inflammation. Some cases of RF are recognized as belonging to the spectrum of immunoglobulin G4-related disease (IgG4-RD). Glucocorticoids are highly effective for treatment of retroperitoneal fibrosis, although the optimal dose and duration of therapy have not been established. An initial dose of prednisone (40-60 mg) daily is usually administered with a tapering scheme. We report on a 55-year-old man diagnosed with IgG4-related RF and successfully treated with a 3-day course of daily 250 mg (4 mg/kg) intravenous methylprednisolone, which resulted in the prompt resolution of urinary obstruction and systemic symptoms.
Use of fludrocortisone for intradialytic hypotension
( Yuri Seo ),( Soomin Jeung ),( Sun-myoung Kang ),( Won Seok Yang ),( Hyosang Kim ),( Soon Bae Kim ) 대한신장학회 2018 Kidney Research and Clinical Practice Vol.37 No.1
Intradialytic hypotension during dialysis adversely affects a patient’s prognosis and increases mortality. We report a case in which intradialytic hypotension that persisted after the administration of midodrine was relieved after the use of fludrocortisone. Administration of 0.2 mg of fludrocortisone occurred 30 minutes before dialysis. We compared 45 sessions of dialysis without fludrocortisone administration and 45 sessions of dialysis with fludrocortisone administration in one patient. The number of times in which systolic blood pressure became lower than 80 mmHg and the number of early terminations of dialysis due to a decrease in systolic blood pressure were higher in the sessions without fludrocortisone administration than in the sessions with fludrocortisone administration (P < 0.05). Fludrocortisone may be helpful for the treatment of intradialytic hypotension that does not respond to midodrine administration.
Multiple System Atrophy Manifested by Bilateral Vocal Cord Palsy as an Initial Sign
Yuri Seo,Soomin Jeung,Heeyoung Yoon,Min-chul Kim,Nah Kyum Lee,Byeong Zu Ghang,Sun Ju Chung,고윤석 대한중환자의학회 2015 Acute and Critical Care Vol.30 No.2
A 71-year-old male initially presented with vocal cord palsy and underwent tracheostomy. After thorough examination, urogenital dysfunction, orthostatic hypotension, and Parkinsonism were found, which led to the diagnosis of multiple system atrophy (MSA). After the tracheostomy, bi-level positive airway pressure ventilation was required during the night due to nocturnal hypoxemia. Nighttime hypoxemia is related to central sleep apnea, which is one of the manifestations of MSA. This is the first case of MSA manifested by bilateral vocal cord palsy as an initial sign in Korea. This case supports the notion that MSA should be taken into consideration when vocal cord paralysis is observed.