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Mammary Paget’s Disease of the Nipple: Relatively Common but Still Unknown to Many
Poh Siang Ooi,Nani Draman,Siti Suhaila Mohd Yusoff,Wan Zainira Wan Zain,Dharmendra Ganasagaran,Hui Heng Chua 대한가정의학회 2019 Korean Journal of Family Medicine Vol.40 No.4
Mammary Paget’s disease is clinically defined as skin inflammation of the nipple area and is an adenocarcinoma of the epidermis of the nipple. The pathogenesis of mammary Paget’s disease is relatively unknown; nonetheless, there are two popular theories that support the underlying carcinoma and de novo carcinogenesis. For the attend-ing medical practitioner, mammary Paget’s disease poses a diagnostic and therapeutic dilemma, especially in the absence of a clinically palpable breast mass. We report a rare case of a 48-year-old Malay woman who presented at Hospital Universiti Sains Malaysia, Kelantan, Malaysia with the symptom of skin erosion on the left nipple and un-responsiveness to multiple topical treatments. A full evaluation and assessment of the patient were conducted, and mammary Paget’s disease was diagnosed.