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Unilateral Multifocal Type 2 Papillary Renal Cell Carcinoma in Adolescence. A Case Report
Sol Yoon(윤솔),Jae Hwi Choi(최재휘),Sin Woo Lee(이신우),Seong Uk Jeh(제성욱),Jeong Seok Hwa(화정석),Jae Seog Hyun(현재석),Ky Hyun Chung(정기현),Hyun Oh Park(박현오),Jong Sil Lee(이종실),See Min Choi(최세민) 대한비뇨기종양학회 2019 대한비뇨기종양학회지 Vol.17 No.1
Papillary renal cell carcinomas (RCCs) can be classified into 2 subtypes (types 1 and 2), depending on their characteristic cytogenetics, immunostaining profiles, and gene-expression profiles. Compared with type 1 papillary RCCs, type 2 papillary RCCs are relatively rare and show more aggressive features. For those reasons, they are associated with a worse prognosis. A 13-year-old patient was admitted to the hospital with right kidney mass. A laparoscopic radical nephrectomy was performed, and results of the histopathologic examination confirmed it to be type 2 papillary RCC. Type 2 papillary RCCs are rarely found in unilateral and multifocal forms, especially in adolescence. Here, we report the unique case of papillary RCC at a young age.