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A Case of Isolated Plexiform Neurofibroma
Ha, Seog Jun,Kim, Jin Wou,Lee, Hyun Jeong,Koh, Bo Kyung 대한피부과학회 2000 Annals of Dermatology Vol.12 No.4
Plexiform neurofibroma is considered to be pathognomic of neurofibromatosis type 1 (NF1). Herein we report a solitary plexiform neurofibroma which is not associated with NF1. A 61-year-old man presented with asymptomatic skin colored nodules on the medial side of his left great toe. No other abnormalities were found in his personal or family history. Clinically, the tumor was simulating the appearance of mucous cysts. Microscopically, it was a plexiform neurofibroma located in the dermis which seemed to originate from small superficial nerves. This case would seem to confirm that the superficial form of plexiform neurofibroma involving small nerves in the dermis or subcutis is not necessarily pathognomic for NF1.
Ha, Seog Jun,Kim, Jin Wou,Lee, Hyun Jeong,Roh, Kee Young 대한피부과학회 1999 Annals of Dermatology Vol.11 No.4
Ota nevus is a dermal melanocytic harmatoma derived from neural crest melanoblast and involves skin innervated by the trigeminal nerve. Although most cases are clinically apparent at birth or around puberty, acquired lesions in adults have been rarely reported. We reported a 73 year-old Korean man with Ota news of the face and scalp that onset in his eighth decade and accompanied multiple solar comedo of the face.
하석준 ( Seog Jun Ha ),권윤희 ( Yoon Hee Kwon ),김태윤 ( Tae Yoon Kim ),김정원 ( Chung Won Kim ) 대한피부과학회 1995 대한피부과학회지 Vol.33 No.3
Reiters syndrome is an unusual disease characterized a triad of nongonococcal urethritis, conjunctivitis, and arthritis in association with the mircoutaneous lesions of keratoderma blenorrhagica and balarintis circinata. We present herein a case of Reiters syndome combined yiti lung cancer. A 39-year-old man has experienced naigrating polyarthralgia and high fever ilitermittently for about 20 years, Hyperkeratotic erythemnous patches and plaques, which dyeliped about 1 year ago, have aggravated and expanded to the whole body. Histopathologic sections from the plaque on the right forc ari showed characteristic findings including thickened parakeratotic horny layer and spongiform micropustules of Kogoji He was associated with HLA-B27. On the chest X-ray, a thumbtip size mass was incidently found. Chest CT and bone scan findings supported lung cancer and multiele metastases. (Kor J Dermatol 1995;33(3): 580-584)
Tegafur 경구 투여후 발생한 선단 홍반 및 색소침착
하석준 ( Seog Jun Ha ),함상희 ( Sang Hee ham ),박영민 ( Young Min Park ),조상현 ( Sang Hyun Cho ),조백기 ( Baik Kee Cho ) 대한피부과학회 1998 대한피부과학회지 Vol.36 No.2
Tegafur is a fluoropyrimidine structurally similar to 5-fluorouracil, used in the treatment of advanced gastrointestinal neoplasms. Mucocutaneous side reactions induced by this agent are rare and include photosensitivity of lichenoid and eczematous types, acral erythema, hyperpigmentation and palmoplantar keratoderma. However, to our knowledge, there has been no report of concurrent development of eruptions of two types in a patient. We describe a female patient with breast cancer, presented with combined features of acral erythema and hyperpigmentation due to oral tegafur. (Korean J Dermatol 1998;36(2) . 363-366)
하석준 ( Seog Jun Ha ),김시용 ( Si Yong Kim ) 대한피부과학회 1996 대한피부과학회지 Vol.34 No.2
Background: This is the first report of study deals with skin tumors in the Suwon and South Kyungiido area during the past 11 years(1983-1993). Objective : We evaluated incidence of tumors, age and sex distribution, and tumor sites. Methods : We reviewed 1506 cases of skin tumors January 1983 to December 1993, at St. Vincent hospital. Results : l. In the 1506 cases of skin tumors, 1280 cases(85.0%) were benign tumors, and 226 cases(15. 0% ) were malignant tumors. 2. Among the 1280 cases of benign tumors, the most common tumor was epidermal cyst, which followed by lipoma, cavernous hemangioma, pilomatricoma, angiolipoma, neurofibroma and sebor rheic keratosis. 3. Among the 226 cases of malignant tumors, 78 cases of basal cell carcinoma, 59 cases of squamous cell carcinoma, 15 cases of malignant melanoma, 11 cases of actinic keratosis and 10 cases of metastatic carcinoma were found. 4. Among the 10 cases of outaneous metastatic cancer, primary sites were lung(3 cases), kidney(3 cases), breast, urinary bladder, stomach and large intestine. Conclusion : The 1506 cases of skin tumors, which were confirmed histologically at the St. Vincent hospital from January 1983 to December 1993, were reviewed. (Kor J Dermatol 1996;34(2): 199-205)