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( Pyoung Jae Park ),( Shin Hwang ),( Young Il Choi ),( Young Dong Yu ),( Gil Chun Park ),( Sung Won Jung ),( Sam Youl Yoon ),( Gi Won Song ),( Tae Yong Ha ),( Sung Gyu Lee ) 대한간학회 2012 Clinical and Molecular Hepatology(대한간학회지) Vol.18 No.4
Erythropoietic protoporphyria (EPP) is an inherited disorder of the heme metabolic pathway that is characterized by accumulation of protoporphyrin in the blood, erythrocytes, and tissues, and cutaneous manifestations of photosensitivity, all resulting from abnormalities in ferrochelatase (FECH) activity due to mutations in the FECH gene. Protoporphyrin is excreted by the liver, and excess protoporphyrin leads to cholelithiasis with obstructive episodes and chronic liver disease, finally progressing to liver cirrhosis. Patients with end-stage EPP-associated liver disease require liver transplantation. We describe here a 31-year-old male patient with EPP who experienced acute-on-chronic liver failure and underwent deceased-donor liver transplantation. Surgical and postoperative care included specific shielding from exposure to ultraviolet radiation to prevent photosensitivity-associated adverse effects. The patient recovered uneventfully and was doing well 24 months after transplantation. Future prevention and treatment of liver disease are discussed in detail. (Clin Mol Hepatol 2012;18:411-415)
Ikchoon Lee,Chul Hyun Kang,Pyoung Sam Park,Hai Whang Lee Korean Chemical Society 1991 Bulletin of the Korean Chemical Society Vol.12 No.3
Kinetic studies of the reactions of benzyl benzenesulfonates with benzylamines in methanol and acetonitrile have been carried out. The reaction was found to proceed by a dissociative $S_N2$ in MeCN but by an associative $S_N2$ mechanism in MeOH. The transition state was rather loose in MeCN whereas it was tight in MeOH, in contrast to a tighter TS in MeCN for the corresponding reactions with aniline. The reaction of benzylamine in MeOH was characteristic of the highly solvated nucleophile, benzylamine, compared to the normal reaction in MeCN.
김종우(Jong Woo Kim),김민식(Min Sik Kim),김평기(Pyoung Gi Kim),노승재(Seung Jae Nor),박찬(Chan Park),조영도(Young Do Jo),박삼규(Sam Gyu Park) 한국암반공학회 2012 터널과지하공간 Vol.22 No.5
본 연구에서는 석회암 지반에서 광산개발이나 토목공사를 수행할 때 데이터베이스로 활용될 수 있는 암석의 기초 물성들을 파악하기 위하여, 제천지역 석회암을 대상으로 수많은 실내 역학시험을 실시하여 암석의 단위중량, 흡수율, 간극률, 탄성파 속도, 쇼어경도, 일축압축강도, 인장강도, 영률, 포와송비, 점착력, 내부마찰각 등의 각종 물리적 성질을 조사하였다. 연구 지역에 분포하는 회색석회암과 이질석회암의 역학적 특성을 비교 검토하였으며, 이질석회암은 회색석회암에 비하여 단위중량은 작고 간극률과 흡수율은 크게 나타나 각종 역학적 특성은 상대적으로 작게 평가되었다. 또한 Mohr-Coulomb 파괴기준과 Hoek-Brown 파괴기준을 적용하여 제천석회암의 파괴조건을 해석하였으며, 여러 가지 물성간의 단순회귀분석과 다중회귀분석을 통해 물성 상호간의 관련성을 알아보았다. In order to evaluate the physical properties of rock which might serve as a database for both mining and civil works, a lot of laboratory tests for Jecheon limestones were conducted to find unit weight, absorption ratio, porosity, elastic wave velocity, uniaxial compressive strength, Young"s modulus, poisson"s ratio, tensile strength, shore hardness, friction angle and cohesion. On investigation of the mechanical properties of both the gray limestone and the clayey limestone distributed in the studied region, the clayey limestone turned out to have more weak mechanical properties which might come from low unit weight, high absorption ratio and high porosity of rocks. The failure criteria of Jecheon limestones were discussed by means of both Mohr-Coulomb criterion and Hoek-Brown criterion. Regression analyses of the physical properties obtained from a lot of laboratory tests were also conducted by means of both linear and multiple regression analyses.