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McGrath, Kimberly M.,Prakash, G. K.Surya,Olah, George. A. 한국공업화학회 2004 Journal of Industrial and Engineering Chemistry Vol.10 No.7
Over the past 15 years, the electrical performance of direct methanol fuel cells (DMFCs) has increased at least tenfold. With this advancement, portable DMFC-powered devices have come to fruition along with dramatic improvement in small power plant and transportation applications. While the DMFC has a theoretical energy density of 6094 W h/kg, only 1000-3200 W h/kg of this energy is realized in practice. Although most portable power applications only necessitate several W h/kg, performance and cost issues associated with polymer electrolyte membranes (PEMs), anode and cathode catalysts, system design, and operational considerations must be overcome for DMFCs to have a role in the methanol economy. This review covers mostly the chemistry aspects of DMFCs.
Recently Identified Forms of Epidermolysis Bullosa
( John A. Mcgrath ) 대한피부과학회 2015 Annals of Dermatology Vol.27 No.6
Epidermolysis bullosa (EB) comprises a collection of clinically diverse inherited blistering diseases that affect the skin and, in some subtypes, mucous membranes and other organs. Currently classified into four main subtypes (EB simplex, junctional EB, dystrophic EB, and Kindler syndrome, mainly based on the level of skin cleavage), the spectrum of EB extends to more than 30 clinical subtypes with pathogenic mutations in at least 18 distinct genes. This review focuses on three recent additions to variants of EB: all are auto-somal recessive, and result from mutations in either DST-e(coding for epidermal dystonin, also known as the 230 kDa bullous pemphigoid antigen, BP230), EXPH5 (coding for exophilin-5, also known as Slac2-b), or ITGA3 (coding for the integrin alpha-3 subunit). Each of these new forms of EB is reviewed with respect to the initial gene discovery, clinical features, the current mutation database, and skin pathology. Awareness of these recently described forms of EB is helpful in the clinical evaluation of patients with EB and in defining genotype-phenotype correlation for inherited blistering skin diseases. (Ann Dermatol 27(6) 658∼666, 2015)