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Sabina Vasaturo,David E. Ploeg,Guadalupe Buitrago,Katja Zeppenfeld,Maud Veselic-Charvat,Lucia J.M. Kroft 대한영상의학회 2015 Korean Journal of Radiology Vol.16 No.3
A 53-year-old woman was referred for ventricular fibrillation with resuscitation. A CT-angiography showed signs of a right ventricular enlargement without obvious cause. A cardiac MRI demonstrated a dilated and hypokinetic right ventricle with extensive late gadolinium enhancement. Arrhythmogenic right ventricular dysplasia (ARVD) was suspected according to the “revised ARVD task force criteria”. An endomyocardial biopsy was inconclusive. The patient developed purulent pericarditis after epicardial ablation therapy and died of toxic shock syndrome. The post-mortem pathologic examination demonstrated sarcoidosis involving the heart, lungs, and thyroid gland.