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A Case of Acute Encephalopathy in Respiratory Syncytial Virus Sepsis Syndrome
유철우(Chur Woo You),이수진(Soo Jin Lee),곡진진(Chen Chen Chu),김현정(Hyun Jung Kim),김승연(Seung Yeon Kim),남지우(Ji woo Nam),김존수(Jon Soo Kim),강주형(Ju Hyung Kang) 대한소아신경학회 2015 대한소아신경학회지 Vol.23 No.2
호흡기 세포융합 바이러스(RSV)는 소아에서 급성 호흡기 감염을 일으키는 가장 흔한 바이러스중 하나로 대부분 경한 호흡기 증상을 일으킨 후 호전 보이지만 1%에서는 중증의 임상경과를 보인다. 중증 RSV 감염에서 호흡기 증상과 동반된 호흡기외 증상이 더 자주 보고되고 있으나 이와 관련된 뇌증에 대한 보고는 많이 알려지지 않았다. 저자들은 미숙아로 출생하여 기관지폐이형성증을 기저질환으로 갖고 있는 8 개월 남아가 RSV에 감염되어 급성 뇌증을 일으켰고 이후 패혈증 증후군으로 진행되었다가 면역글로불린 치료 후 회복되었지만 신경학적 후유증이 남게 된 증례를 보고하고자 한다. Respiratory syncytial virus (RSV) is the most common and important etiologic agent of early childhood respiratory infections, resulting in significant morbidity and mortality. Extrapulmonary manifestations combined with respiratory symptoms are being reported more frequently in severe RSV infection, but the encephalopathy associated with this infection is not well recognized. RSV encephalopathy was present with impaired consciousness, cyanosis, sucking disorder preceding convulsive seizures. The authors describe the symptoms and outcomes of an 8monthold boy, who present with acute encephalopathy and had prematurity, bronchopulmonary dysplasia as comorbidities. The boy developed sepsis syndrome, characterized by hypotension, hepatic and renal dysfunctions, later found to be infected with RSV. He finally recovered after treatment with immumoglobulin and supportive care but required portable mechanical ventilation, nasogastric tube feeding, and anticonvulsant medication at discharge.
A pediatric case of idiopathic Harlequin syndrome
Kim, Ju Young,Lee, Moon Souk,Kim, Seung Yeon,Kim, Hyun Jung,Lee, Soo Jin,You, Chur Woo,Kim, Jon Soo,Kang, Ju Hyung The Korean Pediatric Society 2016 Clinical and Experimental Pediatrics (CEP) Vol.59 No.no.sup1
Harlequin syndrome, which is a rare disorder caused by dysfunction of the autonomic system, manifests as asymmetric facial flushing and sweating in response to heat, exercise, or emotional factors. The syndrome may be primary (idiopathic) with a benign course, or can occur secondary to structural abnormalities or iatrogenic factors. The precise mechanism underlying idiopathic harlequin syndrome remains unclear. Here, we describe a case of a 6-year-old boy who reported left hemifacial flushing and sweating after exercise. He had an unremarkable birth history and no significant medical history. Complete ophthalmological and neurological examinations were performed, and no other abnormalities were identified. Magnetic resonance imaging was performed to exclude lesions of the cerebrum and cervicothoracic spinal cord, and no abnormalities were noted. His final diagnosis was classic idiopathic harlequin syndrome. Herein, we report the first pediatric case of idiopathic harlequin syndrome in Korea.
A pediatric case of idiopathic Harlequin syndrome
Ju Young Kim,Moon Souk Lee,Seung-Yeon Kim,Hyun Jung Kim,Soo Jin Lee,Chur Woo You,Jon Soo Kim,Ju Hyung Kang 대한소아청소년과학회 2016 Clinical and Experimental Pediatrics (CEP) Vol.59 No.no.sup1
Harlequin syndrome, which is a rare disorder caused by dysfunction of the autonomic system, manifests as asymmetric facial flushing and sweating in response to heat, exercise, or emotional factors. The syndrome may be primary (idiopathic) with a benign course, or can occur secondary to structural abnormalities or iatrogenic factors. The precise mechanism underlying idiopathic harlequin syndrome remains unclear. Here, we describe a case of a 6-year-old boy who reported left hemifacial flushing and sweating after exercise. He had an unremarkable birth history and no significant medical history. Complete ophthalmological and neurological examinations were performed, and no other abnormalities were identified. Magnetic resonance imaging was performed to exclude lesions of the cerebrum and cervicothoracic spinal cord, and no abnormalities were noted. His final diagnosis was classic idiopathic harlequin syndrome. Herein, we report the first pediatric case of idiopathic harlequin syndrome in Korea.