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속립성 뇌결핵의 초기 자기공명영상 소견과 치료 후 변화
장재호,임재우,정순이,최규철,한태일,Jang, Jae Ho,Lim, Jae Woo,Jung, Soon Lee,Choeh, Kyuchul,Han, Taeil 대한소아청소년과학회 2002 Clinical and Experimental Pediatrics (CEP) Vol.45 No.12
저자들은 속립성 결핵으로 진단한 23개월된 여아에서 신경학적인 증상이 나타나기 전인 초기의 속립성 뇌결핵에서 뇌자기공명영상 소견 및 치료에 따른 경시적 호전 양상의 변화를 자기공명영상소견으로 얻었기에 보고하는 바이다. A 23-month-old girl visited with chronic cough and her chest radiograph showed miliary tuberculosis. There was no neurological abnormality. But CSF findings showed WBC $22/mm^3$(lymphocyte 20%, neutrophil 80%) and positive result of polymease chain reaction(PCR) for M. tuberculosis. MR imaging showed multiple ring enhanced nodules and ovoid nonenhancing bright signal lesion on the cerebrum, cerebellar parenchyme, and left basal ganglia. Antituberculous chemotherapy was done and follow-up MR imaging was done after six months. One month after treatment, the number and size of nodules had decreased. Six months after treatment, the multiple enhanced nodules and leptomeningeal enhancement were not observed, and high signal intensity of genu portion of left internal capsule and posterior portion of putamen were decreased.
특발성 혈소판 감소성 자반증에서 정주용 감마 글로불린의 투여 방법에 따른 효과 비교
장재호,이문숙,박미라,최규철,Jang, Jae Ho,Lee, Moonsouk,Park, Mira,Choeh, Kyuchul 대한소아청소년과학회 2003 Clinical and Experimental Pediatrics (CEP) Vol.46 No.4
목 적 : 자가면역질환에서 정주용 감마글로불린(IVG)의 투여법은 여러 가지가 있으나 크게 2가지로 대별되며 400 mg/kg/일 5일간 투여법과 2 g/kg/일 1일간 투여법이 있고, 이 두가지 요법의 치료성적의 차이점이 각 자가면역질환별로 밝혀지고 있으나 ITP에서는 어느 치료법이 보다 효과적인지에 대해 아직 밝혀져 있지 않다. 이에 두가지 치료법의 반응 속도, 부작용, 재발율 등의 치료효과를 비교하고자 본 연구를 시도하였다. 방 법 : 1995년 1월부터 2001년 6월까지 을지대학병원 소아과에 입원한 ITP환아 47명에 대해 IVG 2 g/kg/일 1일간 정맥투여법(A요법)과 400 mg/kg/일 5일간 정맥투여법(B요법)을 무작위로 선택하여 A요법군 25명과 B요법군 22명에 대해 치료효과를 전향적으로 조사하였다. 결 과 : 1) A요법군에서 혈소판이 빨리 증가하여 치료 시작 2, 4, 6일에 의미 있는 차이를 보였다. 2) A요법군이 오한, 발열, 구토 같은 부작용이 많았으나 치료를 중단할 만한 심한 부작용은 없었다. 3) 치료 부작용이 있는 경우 치료 6일째의 혈소판 수가 의미있게 많았다. 4) 재발율에는 두 요법군 사이에 차이가 없었다. 결 론 : 혈소판 감소성 자반증일 때 뇌출혈은 발병 초기 7일이내에 잘 발생하므로 중증 출혈을 막고자 한다면 면역글로불린 투여를 2 g/kg/일 1일간 정맥투여법으로 하는 것이 유리하리라고 사료된다. Purpose : Several methods of IV ${\gamma}-globulin$(IVG) infusion are effective in the treatment of autoimmune disease, including idiopathic thrombocytopenic purpura(ITP). But it is not known which method is more effective in the treatment of ITP. The effectiveness of these two methods of IVG infusion was studied in terms of platelet recovery rate, side effects and recurrence rate. Methods : Forty seven patients with acute ITP in the department of pediatrics, Eulji University Hospital from January 1995 to June 2001 were enrolled. We assesssed the treatment effects of 47 patients blindly selected; IV ${\gamma}-globulin$ 2 g/kg/day in one day(treatment group A, n=25), 400 mg/kg/day in five days(treatment group B, n=22). Results : Treatment group A increased platelet count more rapidly on the 2nd, 4th and 6th day of treatment than treatment group B. Side effects like fever, chill and vomiting were more frequent in treatment group A than treatment group B. The platelet count on the sixth day of treatment showed a greater increase in the cases which had side effects than in the cases which did not. There was no difference between the two groups in the recurrence rate. Conclusion : IV ${\gamma}-globulin$ 2 g/kg/day in one day increases platelet count more rapidly than 400 mg/kg/day in five days, and is favorable for the prevention of a severe hemorrhagic episode like early intracranial hemorrhage.
김선준(Sun Jun Kim),송명숙(Myoung Sook Song),최규철(Kyuchul Choeh) 대한소아신경학회 1995 대한소아신경학회지 Vol.2 No.2
We experienced two cases of neurofibromatosis type 1 with cerebellar astrocytoma in 6-year-old and 14-year-old boys. They had multiple cafe-au-lait spots. Lisch nodule and neurofibromas with cerebellar astrocytoma. The excision of the tumor mass and radiotherapy was done in the former patient and he recovered without neurolongic seguelae, but the other patient had discharged without any therapy. A brief rewiew of literatures was also presented.
배웅직(Woung Jik Bae),강의자(Yee Ja Kang),김선준(Sun Jun Kim),최규철(Kyuchul choeh) 대한소아신경학회 1995 대한소아신경학회지 Vol.2 No.2
We observed clinical features of 36 neonatal hypoglycemic patients who was admitted to the neonatal cere unit in the pediatric department of Tae Jeon Eul Ji Hospital during the period from April 1994 to February 1995. The result are as follows : 1) The incidence of neonatal hypoglycemia was 1.2%. Male to female ratio were 1:1.12. 2) The most frequent cause of neonatal hypoglycemia was LGA(large for gestational age) (50%) and SGA(small for gestational age)(19%), and followed by LBW(lower birth weight)(5.5%), prematurity(5.5%), sepsis(5.5%), birth asphysia(5.5%), gestational DM(3%), polycythemia(3%), unknown(3%) in order of frequency. 3) The result of EEG finding was normal (41%) and abnormal(59%). In abnormal EEG finding, mild(31.3%), mild to moderate(21.9%), moderate(3.1%) and moderate to markedly abnormal EEG(3.1%) were detected. 4) The mean serum level of hypoglycemic neonate was 24.25±7.64mg/dL in glucose, 2.75±4.69µg/dL, 39.43±24.21 1µU/ml, respectively. 5) Brain sonographic findings were normal(83.2%), mild brain swalling(5.6%), left ventri-cular leukomalasia(2.8%) and mild left ventricular dilatation(2.8%). 6) The finding of AEP(auditory evorked potential) was normal(95.4%) except 1 case(4.6%).