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Pretarsal Motor Persistence의 임상적 특징 및 근전도 소견
주억식,이필휴,이재혁,용석우 대한신경과학회 2005 대한신경과학회지 Vol.23 No.1
Pretarsal motor persistence (PMP), a subtype of apraxia of the eyelid opening, is characterized by the inability to open the eyelids at will due to persistent activity of orbicularis oculi muscles following voluntary closure. Here, we describe clinical characteristic and the synchronous EMG recording from the levator palpebrae and orbicularis oculi muscles of PMP in patient with essential blepharospasm, idiopathic Parkinson's disease, and progressive supranuclear palsy.
인간 골격근세포주(HM4)에서 Interleukin-6 생성에 대한 정맥내 글로불린의 효과
주인수,주억식,김성희,이용범 대한신경과학회 2004 대한신경과학회지 Vol.22 No.3
Background: Intravenous immunoglobulin (IVIg) has been widely used in the management of patients with various autoimmune neurological diseases, however, its action mechanisms have not fully been elucidated yet. This study focused on the effects of IVIg on the production of interleukin-6 (IL-6), one of major proinflammatory cytokine, using a human skeletal muscle cell line (HM4). Methods: After HM4 cells were cultured in Dulbecco's modified eagle's medium (DMEM) containing 5% fetal bovine serum for 24 h, the culture medium was changed with serum-free media. TNF-α (tumor necrosis factor-α, 100 ng/mL) and IVIg (5 mg/mL) were treated alone or in combination and cultured for various time. RT-PCR and ELISA kit were employed for mRNA expression and secretion of IL-6, respectively. Results: Treatment with TNF-α or/and IVIg significantly induced IL-6 mRNA expression (p<0.001). Although IL-6 production was markedly increased by TNF-α (p<0.001), IVIg treatment alone or in combination with TNF-α had no effect on the production of IL-6 except at 6 h after the treatment. Conclusions: IVIg seems not to have a significant effect on IL-6 production as an action mechanism of its immunomodulatory capabilities, at least in the HM4 cell line.