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May-Hegglin Anomaly 산모와 신생아 1 예
김재향 ( Jae Hyang Kim ),김희정 ( Hee Jeong Kim ),김학구 ( Hak Goo Kim ),정영준 ( Young Zoon Jung ) 대한임상검사과학회 2001 대한임상검사과학회지(KJCLS) Vol.33 No.2
May-Hegglin anomaly(MHA) is a rare autosomal dominant disorder. π1Is is the most common type of hereditaη or inherited giant platelet disorders(lGPDs). It is characterized by the presence of giant platelets, thrombocytopenia, abnormal bluish inclusions in the granulocytes, and mild bleeding symptoms. The mechanism of the hemostatic defect is not entirely clear, but bleeding is proportional to the degree of thrombocytopenia. We experienced the mother and neonate affected WIth May-Hegglin anomaly. In the peripheral blood smear, giant platelets and light blue basophilic inclusion bodies in the granulocytes are observed.
항바이러스 치료효과 판정에 대한 간염바이러스청량 검사와 기타 바이러스 항원 검사
문인경 ( In Kyung Moon ),민병해 ( Byung Hae Min ),김인환 ( In Hwan Kim ),김희정 ( Hee Jeong Kim ),김학구 ( Hak Goo Kim ),정영준 ( Young Zoon Jung ) 대한임상검사과학회 2001 대한임상검사과학회지(KJCLS) Vol.33 No.2
Hepatitis-B virus is a serious problem in Korea, and about 7 to 8 % of the populations are in carrier state. The only drugs currently approved for hepatitis-B infection is a -inteferon. However, the cure rate with this treatment is low. Some patients are unresponsive to the interferon, and some relapse when is stopped. Recently, Lamibudine, a novel cytosine analogue, exhibits potent anti-viral activity against hepatitis B virus. The effect of lamibudine treatment is good for almost all patient, but some patients showing refractorlness and the mutant HBV appearance. We studied for what kinds of tests are available for predict the response of lamibudine. HBeAg positive cases are 11.5 % in the HBV -PCR postive group and 0.0% in the HBV-PCR negative group. HBeAg neagtive cases are 88.5% in the HBV-PCR postive group and 100.0% in the HBV-PCR negative group. These results indicate that HBV-PCR test are more reliable for predict the viral state of HBV infection. So the 띠ral status evaluation(infectivity) for HBV infection by HBeAg assay is not recommended. Further studies recruiting on patient’s clinical courses and liver biopsy studies may helpful to determine the HBV viral status.