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코에서 선천성 섬유상피폴립이 피부뿔로 발현한 환자 증례보고
권용석(Yongseok Kwon),전동근(Dongkeun Jun),이명철(Myungchul Lee),최현곤(Hyungon Choi),신동혁(Donghyeok Shin),김지남(Jeenam Kim) 대한두경부종양학회 2020 대한두경부 종양학회지 Vol.36 No.2
Cutaneous horn is the clinical entity, which is circumscribed, conical, markedly hyperkeratotic lesion in which the height of the keratotic mass amounts to at least half of its largest diameter. It may be associated with many different pathological lesions. It is a relatively rare and a kind of epidermal tumor that generally appears as a conical projection. Here, we report rare case of congenital cutaneous horn. A 39-month-old female Korean patient presented at our clinic with a mass at the tip of her nose present since birth. Under general anesthesia, cutaneous horn of nasal tip was completely excised without any complications. The operation site was small enough to perform a primary closure, without any nasal deformity. Histopathologically, it was reported as a fibroepithelial polyps. After operation, there is no evidence of recurrence at 16 months of follow-up.
색소피부건조증 환자에서 발생한 안면부 기저세포암의 치료 증례 보고
배재현(Jaehyun Bae),전동근(Dongkeun Jun),김지남(Jeenam Kim),이명철(Myungchul Lee),신동혁(Donghyeok Shin),임소덕(So Dug Lim),최현곤(Hyungon Choi) 대한두경부종양학회 2020 대한두경부 종양학회지 Vol.36 No.1
Xeroderma pigmentosum is a rare autosomal recessive disease, related to defects in DNA repair mechanism. It presents skin lesions on sun-exposed areas, leading to various skin cancer. Skin lesions can be treated with cryotherapy, skin resurfacing, 5-FU, Imiquimod, topical T4 endonuclease V, radiotherapy and genetic therapy, but invasive skin cancer should be treated by a surgery. We report a 12-year-old female xeroderma pigmentosum patient with recurrent basal cell carcinoma successfully treated by skin grafting. In that there is no cure for this disease, prevention and patient education is most important.
정민경(Minkyoung Jeong),권용석(Yongseok Kwon),전동근(Dongkeun Jun),이명철(Myungchul Lee),김지남(Jeenam Kim),신동혁(Donghyeok Shin),김완섭(Wan-seop Kim),최현곤(Hyungon Choi) 대한두경부종양학회 2021 대한두경부 종양학회지 Vol.37 No.1
Intraosseous hemangioma is a rare, benign vascular tumor of endothelial origin. It accounts for fewer than 1% of all hemangiomas, and very rarely occurs in the face. Intraosseous hemangioma usually presents as an asymptomatic lesion, but symptoms can occur due to the mass effect. The authors describe a case of intraosseous hemangioma of the zygoma with a review of the relevant literature. A 44-year-old man presented with a chief complaint of painless swelling on the left zygomatic region that had been slowly growing for the past year. On physical examination, a hard, non-movable mass in a deep layer was palpated. On computed tomography performed to evaluate its layers and extent, trabeculation was found inside the mass, but the lack of destruction of the surrounding bone suggested that the mass was benign. Complete surgical excision was performed under local anesthesia. After complete excision of the mass, slight erosions remained on the cortical bone of the zygoma, but because it was small enough not to cause a facial deformity such as depression or asymmetry, no additional reconstructive procedure was performed. There were no symptoms or recurrence during a 8-month follow-up period.