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원자 폭탄 피해자의 후손에서 발생한 색소성 건피증과 각막 편평상피세포암 1예
이동초(Dong Cho Lee),최웅산(Woong San Choi),안정현(Jung Hyun Ahn) 대한검안학회 2007 Annals of optometry and contact lens Vol.6 No.1
목적: 원자폭탄 피해자의 후손에서 발생한 색소성 건피증 환자에서 각막 종양이 동반된 예를 경험하였기에 이를 보고하는 바이다. 대상과 방법: 15세경 색소성 건피증 진단을 받은 과거력이 있는 45세 남자 환자가 좌안의 시력 저하를 주소로 내원하였다. 가족력상 부친이 일본 히로시마에서 원자폭탄 피폭의 병력이 있었으며, 친형도 환자와 같은 색소성 건피증을 앓았다고 하며, 환자는 색소성 건피증과 더불어 안면부에 다발성 편평상피세포암이 동반되어 타 병원에서 수차례 수술을 받은 과거력이 있었다. 좌안 시력은 0.3이었고, 좌안 각막 이측에 3×6 mm 크기의 백색의 종괴와 내측 각막 주변부의 혼탁이 관찰되었으며 내측과 외측 결막에 익상편과 유사한 결막 증식과 결막 충혈을 보였으며 각막 종괴를 제거하였고, 증식된 결막을 절제한 후 양막이식술을 시행하였다. 결과: 각막 종괴의 조직 병리소견상 편평상피세포암으로 확인되었다. 술 후 1년 뒤에도 결막 및 각막에 종양 조직의 재발 없이 치유되었으며 환자의 시력은 0.6으로 호전되었다. Purpose: To report a case of corneal squamous cell carcinoma and Xeroderma pigmentosum in the offspring of atomic bomb survivor. Methods: A 45-year old male diagnosed with Xeroderma Pigmentosum at the age of 15 years presented with decreased visual acuity of his left eye. His brother also had Xeroderma Pigmentosum. His father was atomic bomb survivor in Hiroshima. Multiple squamous cell carcinoma affected right eye which was developed on his face starting from the age of 15 years, and were treated by local excision and exentration at other hospital. On his first visit to our hospital, his left visual acuity was 0.3. The left eye revealed 3×6 mm sized, whitish mass on temporal cornea, and corneal opacity on nasal cornea with pterygium-like growth. The excision of the pterygium-like lesion and corneal mass was done. Amniotic membrane was sutured with 10-0 nylon to cover the bare sclera fully. Results: The pathologic result was consistent with the diagnosis of squamous cell carcinoma in situ. During the one year follow-up, neither recurrence nor any postoperative complication. We found postoperative best corrected visual acuity improved from 0.3 to 0.6 after one year.
1시간이상 떨어진 다발성 망막열공에 의한 망막박리 환자에서 기체망막유착술을 시행한 3예
조우형,이동초,장무환.Woo-Hyung Cho. M.D.. Dong-Cho Lee. M.D.. Moo-Hwan Chang. M.D. 대한안과학회 2005 대한안과학회지 Vol.46 No.12
Purpose: To determine the effects of performing pneumoretinopexy in patients without the conventional indication of pneumoretinopexy but with rhegmatogenous retinal detachment by multiple retinal tears separated over 1 hour in distance. Methods: Three patients with rhegmatogenous retinal detachment by multiple retinal tears separated over 1 hour in distance from November 2003 to December 2003 were the subject of this study. Treatment records of the patients were examined retrospectively. In one case, when performing pneumoretinopexy, 0.5 cc of vitreous was aspirated followed by an injection of 0.8 cc SF6 gas. In the other two cases, after injecting 0.5 cc of SF6 gas, one retinal tear was adhered in the proper position. Then, sequential retinal adhesion was attempted by changing the position. Results: In all three cases, anatomical retinal adhesion was maintained, and visual acuity functionality was improved. Conclusions: Both sequential retinal adhesion by changing the position and performing pneumoretinopexy after vitreous aspiration are successful method of retinal adhesion. Therefore, pneumoretinopexy can be used as an effective medical treatment in patients with rhegmatogenous retinal detachment by multiple retinal tears separated over 1 hour in distance.
이명원,이동초,장무환.Myung Won Lee. M.D.. Dong Cho Lee. M.D.. Moo Hwan Chang. M.D. 대한안과학회 2007 대한안과학회지 Vol.48 No.7
Purpose: This clinical report describes the characteristics and ophthalmic treatment of a patient with anhidrotic ectodermal dysplasia showing bilateral upper eyelid entropion, conjunctival mass and dry eye syndrome. Methods: A 12-year-old boy presented to our clinic complaining of a white mass on the lower tarsal conjunctiva, foreign body sensation, and an itching in his right eye of one-year duration. He had developmental defects in his hair, teeth, nails and sweat glands. He had dry skin, a flat upper-lip, heat intolerance, a saddle-backed nose, and hypohidrosis. Ophthalmic examination showed blepharitis, a conjunctival mass, and bilateral upper eyelid entropion. Results: Upper eyelid entropion surgery was performed. An excisional biopsy of the conjunctival mass showed nonspecific acute and chronic inflammation. Conclusions: We concluded that the conjunctival mass developed as a result of chronic inflammation caused by chronic conjunctivitis and dry eye syndrome. Regular lid-hygiene with swab and lubrication is useful to minimize recurrent ocular inflammation in anhidrotic ectodermal dysplasia.
미세각막절삭기를 이용한 라식 수술 시 각막절편 두께에 영향을 미치는 수술 전 인자
조우형,이동초,장무환,Woo Hyung Cho,Dong Cho Lee,Moo Hwan Chang 대한안과학회 2006 대한안과학회지 Vol.47 No.4
Purpose: To identify factors that may be related to variations in corneal flap thickness in LASIK using the Moria M2 microkeratome. Methods: The charts of patients having LASIK based on steep keratometry nomogram using Moria M2 microkeratome (head : 110 ?m) and excimer laser (VISX STAR S2, USA) in our department of ophthalmology from March, 2003, to May 2005, were reviewed retrospectively. A total of 195 eyes were enrolled in the investigation. We analyzed relationship between corneal flap thickness and preoperative factors including central corneal thickness, steep keratometer, corneal diameter, suction ring using multiple regression analysis. Results: Mean corneal flap thickness was 119.37±21.21 ?m. There was a statistically significant positive correlation between flap thickness and central corneal thickness (p<0.05). No correlation was found between flap thickness and other preoperative factors including steep keratometer, corneal diameter and suction ring. Conclusions: Mean corneal flap thickness using the Moria M2 110 ?m head was 119.37±21.21 ?m, little thicker than our expectation. When surgery is performed based on steep keratometry nomogram using Moria M2 microkeratome, if intraoperative factors are excluded, there is a trend toward thicker flap thickness with thicker central corneal thickness, whereas steep keratometer, corneal diameter or suction ring have no influence on flap thickness.
이명원,안정현,경성은,이동초,Myung Won Lee,Jung Hyun Ahn,Sung Eun Kyung,Dong Cho Lee 대한안과학회 2007 대한안과학회지 Vol.48 No.9
Purpose: The purpose of this case report is to describe accompanying ocular findings, especially optic neuropathy, in a patient with MELAS syndrome. Methods: A 10-year-old male patient who had lactic acidosis and neurological symptoms (loss of consciousness, vomiting, epilepsy, decreased vision, and constricted visual field), underwent a brain magnetic resonance imaging (MRI) scan and a molecular genetic analysis. Results: A diagnosis of cerebral infarction due to occlusion in the right posterior cerebral artery was made and confirmed by MRI scan. The diagnosis of MELAS syndrome was confirmed by performing molecular genetic analysis demonstrating the transformation of the mitochondrial tRNAleu(UUR) gene (MTTL1) A to G(3243). According to the ocular examinations, the patient??s left eye showed decreased vision, hemianopsia, relative afferent pupillary defects, mild swelling of optic nerve, and decreased amplitude on visual evoked potential exam. Conclusions: We encountered a case of MELAS syndrome involving optic neuropathy, which can (although rarely) occur with this syndrome. Therefore, in patients with an optic neuropathy of uncertain etiology, clinicians should consider performing comprehensive ocular exams and molecular genetic exams to rule out the possibility of genetic diseases.