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은철,이창우 ( Ehul Eun,Chang Woo Lee ) 대한피부과학회 1997 大韓皮膚科學會誌 Vol.35 No.5
Background: Localized scleroderma, a rare autoimmune disease, can be classified into three subtypes.linear scleroderma, morphea and generalized morphea. Localized scleroderma is usually limited to the skin and subcutaneous tissue but may result in permanent functional disability. Because of its rarity, there are few large scale clinical studies of pediatric patients with localized scleroderma in Korea. Objective : In this study we have examined 11 Korean pediatric patients with localized scleroderma registered at Hanyang university hospital. A review of the clinical presentation, laboratory data, therapy and complcations was carried out in detail. Methods : The medical records of 11 pediatric patients with localized scleroderma seen at the department at Hanyang University Hospital, between 1990 and 1996, were reviewed. The diagnoses were classified into one of the above three localized scleroderma subtypes based on the results of the physical examination, and all patients were examined periodically. The clinical features of the disease, laboratory results, treatment modalities, and complications were summerized from the review of the records. Results : Among the 11 patients, 8 were female and 3 were male; 7 had morphea and 4 had linear scleroderma. The average age at onset was 8.6 years. Antinuclear antibodies above the titer of 1:40 were present in 36%. One of 3 patients with linear scleroderma which involved the upper extremities had moderate degrees of joint contracture. Ten of 11 patients were treated with intralesional injection of corticosteroid and oral medications of hydroxychloroquine, prednisolone and/or nosteraidal anti-inflammatory drugs. Conclusion : Localized scleroderma has no recognized internal organ involvements and is not thought to progress to systemic sclerosis. Since localized scleroderma may cause complications from local atrophy to joint contractures, patients will need to take adequate treatment. and fol- low-up examinations. (Korean J Dermatol 1997;35(5): 877-882)
Dapsone으로 치료한 안면 파종상 속립성 루프스 2예
은철 ( Chul Eun ),이창우 ( Chang Woo Lee ) 대한피부과학회 1996 대한피부과학회지 Vol.34 No.6
Lupus miliaris disseminatus faciei (LMDF) is an asymptomatic papular eruption affecting the central area of the face. It runs a chronic course and can involute spontaneously with scarring. The treatment of LM~BF has not been satisfactory despite the use of many different kinds of topical and systemic agents. In the early 1980s, Kumano et al. reported their experiences with this disease using dapsone : the efficacy of dapsone was described as excellent. With this report in mind, we have used dapsone(50-100mg/d) in 2 patients with LMDF, and a marked irnprovement or almost cure of the skin disease were recognized. (Kor J Dermatol 1998;34(6): 1016-1020)
은철 ( Chul Eun ),노영석 ( Young Suck Ro ),이창우 ( Chang Woo Lee ) 대한피부과학회 1996 대한피부과학회지 Vol.34 No.4
Isotopic response is the occurrence of a new unrelated disease that appears at the same location as a previously already healed disease. In 1995, Wolf et al defined a this new phenomenon and reported eight new cases with fiftyeight cases corresponding to the definition for this phenomenon in literiture. We report two cases considered as isotopic response, urticarial vasculitis and erythema multiforme developed on striae distensae, respectively. (Kor J Dermatol 1996;34(4): 664-667)