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강병덕,양재석,김일환,송해준,오칠환 ( Byung Duk Kang,Jae Seok Yang,Ill Hwan Kim,Hae Jun Song,Chil Hwan Oh ) 대한피부과학회 1997 대한피부과학회지 Vol.35 No.1
Reactive perforating collagenosis(RPC) is a rare perforating disorder characterized by transepithelial elimination of altered collagen. Two types of RPC occur:inherited and acquired. The acquired type arises during adult life without a familial tendency. It is accompanied by scratching and usually is associated with diabetes mellitus, chronic renal failure, lymphoma and AIDS. We report three cases of the acquired form of RPC. Pruritus was the common factor among them. In two patients, chronic renal failure and hyperthyroidism were associated with RPC. Histopathological and ultrastructural findings showed transepithelial elimination of collagen. Control of itching was helpful for clearing the lesions.(Kor J Dermatol 1997;35(1):204∼208)
A Case of Cutis Marmorata Telangiectatica Congenita
홍진호,김동준,홍영숙,오칠환,강병국 대한피부과학회 1996 Annals of Dermatology Vol.8 No.1
Cutis marmorata telangiectatica congenita(CMTC) is a rare congenital cutaneous vascular anomaly. The major shin findings are persistent, fixed crabs marmorata, telangiectasia, and phlebectasla. In approximately 50% of patients, the bier tends to be associated with various congenital anomalies. We describe in the report a 4-month-old male infant with CMTC. The patient had red or violet marbled patches, telangiectatses, and atrophy on the right arm present at birth. During the follow up period of 12 months, there was no change in the cutis marmorata pattern and telangiectases, whereas the atrophy has-been less prominent than at the initial visit