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내시경적 절제술로 치료된 바터팽대부의 동시 발현된 신경절세포부신경절종과 이소성 췌장 1예
강균은 ( Gyoun-eun Kang ),김현수 ( Hyunsoo Kim ),이재광 ( Jae Kwang Lee ),김동현 ( Dong Hyun Kim ),정비나 ( Bi-na Jeong ),장지훈 ( Ji-hun Jang ),여상명 ( Sang-myung Yeo ),손경락 ( Kyung-rak Sohn ) 대한췌담도학회 2016 대한췌담도학회지 Vol.21 No.4
저자들은 상복부 불편감으로 발견된 바터팽대부 점막하종양의 진단과 치료를 위해 시행한 내시경적 절제술상 신경절세포 부신경절종과 이소성 췌장이 동시 발현된 증례를 경험하여 문헌고찰과 함께 보고하는 바이다. Gangliocytic paraganglioma is an uncommon tumor of digestive system that is usually found in the second portion of duodenum. It is generally considered benign tumor, although few reports of local recurrences and regional lymph node metastases have been made. Gangliocytic paraganglioma is characterized by its histologic pattern including ganglion cells, spindle cells and epithelioid cells. Heterotopic pancreas, also known as ectopic pancreas, is a pancreatic tissue appeared outside of its normal location lacking anatomic or vascular connection with the pancreas. In duodenum, it is a relatively unusual lesion that may be found incidentally during surgery or endoscopy. We present a case of 39-year-old woman with gangliocytic paraganglioma combined with heterotopic pancreas in the ampulla of Vater successfully treated by endoscopic resection.