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유지원 ( Ji Won Ryu ),남승우 ( Seong Woo Nam ),권혁춘 ( Hyuck Choon Kweon ),최승준 ( Song Jun Choi ),김상용 ( Sang Young Kim ),박현미 ( Heun Mi Park ),안혜선 ( He Sun An ) 전북대학교 의과학연구소 2010 全北醫大論文集 Vol.34 No.2
저자들은 만성 설사와 하지 부종을 주소로 내원한 63세 여자 환자에서 류마티스 관절염과 연관되고 대장에 국한된 속발성 유전분증을 진단하였고 환자의 임상경과를 기존의 문헌 고찰과 함께 보고하는 바이다. Suspicion of gastrointestinal amyloidosis in patients without known history of amyloidosis is difficult, but gastrointestinal amyloidosis should be considered in those older than 30year with unexplained diarrhea, weight loss or malabsorption. We experienced a case of an 63-year-old female in patient with rheumatoid arthritis, who have a chronic watery diarrhea caused by colonic amyloidosis. Congo-red stain and immunohistochemical stain for amyloid A protein of colonoscopic pathologic specimen showed positive response. Other organs such as kidney, heart, liver and skin, were not involved by amyloidosis. She was diagnosed to secondary and localized colonic amyloidosis related with rheumatoid arthritis. In spite of anti-rheumatic therapy, our patient did not recover.