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8개월 영아의 좌측 이하선 부위에서 발생한 배아형 횡문근육종 1예
조민혁(Minhyuk Cho),김연수(Yeon Soo Kim),신유섭(YooSeob Shin),김철호(Chul-Ho Kim) 대한두경부종양학회 2014 대한두경부 종양학회지 Vol.30 No.2
Rhabdomyosarcoma is the most common sarcoma in children less than 15 years of age. Two major histological subtypes are embryonal and alveolar. Embryonal rhabdomyosarcoma is diagnosed by immunopathology and treat-ments require coordinated management plans that include surgery, chemotherapy, and usually radiotherapy. 8-month-old male infant visited with swelling in left parotid area. Computed tomography scan showed a hetero- geneous mass in the left parotid area and the result of fine-needle aspiration cytology was suspicious malignancy. Left total parotidectomy was performed and CSF leakage was noted and repaired. Confirmed by positive reactions to desmin and myogenin, the diagnosis was embryonal rhabdomyosarcoma. On postoperative brain MRI, extension along the meninges was noted and for treatment, chemotherapy and gamma knife radiosurgery were done. Five years after initial surgical resection(3 years and 10 months after completion of chemotherapy and gamma knife radiosurgery), the child did not show any evidence of local recurrence or distant metastasis.
기관을 침범한 유두상 갑상선 암 환자에서 흉설골근을 통한 기관재건술 1예
우희원(Hee Won Wu),김연수(Yeon Soo Kim),신유섭(YooSeob Shin),김철호(Chul-Ho Kim) 대한두경부종양학회 2014 대한두경부 종양학회지 Vol.30 No.2
Papillary thyroid carcinoma is known as its relatively high cure rate after surgical treatment. But invasion of the trachea by thyroid carcinoma is poor prognostic factor and the best management is en bloc surgical resection of the tumor invading the trachea. A 55-year-old man was diagnosed as papillary thyroid cancer with tracheal in-vasion. We treated the patient by total thyroidectomy with window resection of invading trachea followed by im- mediate reconstruction with sternohyoid muscle flap and tracheostomy. At 48 days after surgery, tracheostoma was closed and the patient had no functional complication by the surgical process. Until 10 months after surgery, there was no sign of recurrence and the patient led social life without any discomfort. We present this case with a review of the related literatures.