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송준환(Joon Hwan Song),선동신(Dong Shin Sun),김호(Ho Kim),이윤희(Yoon Hee Lee),홍용희(Yong Hee Hong),이동환(Dong Hwan Lee) 대한의학유전학회 2009 대한의학유전학회지 Vol.6 No.1
저자들은 출생당시 특이소견 없었고, 유전질환의 가족력이 없는 20세 남자 환자에서 우측하지에 골전이가 동반된 횡문근육종을 발견하고, 저신장, 탈모, 백내장, 치열이상, 골다공증, 갑상선기능저하증, 작은 손과 발, 사지는 가늘고 체간이 두터우며, 신체에 비해 큰 머리등 특이한 외모를 가진 워너증후군으로 진단한 1례를 경험하였기에 문헌 고찰과 함께 보고하고자 한다. Werner syndrome (WRN), or adult progeria, is a very rare, autosomal recessive disorder characterized by the appearance of accelerated aging, including cataracts, gray hair, skin atrophy, and atherosclerosis. This syndrome is caused by mutations in the WRN gene and had a high risk of a spectrum of rare neoplasms including: i) non-epithelial malignant or pre-malignant tumors/conditions, osteosarcomas and soft tissue sarcomas, malignant melanomas, myeloid leukemia and myelodysplastic syndrome; ii) an epithelial neoplasm, thyroid carcinoma, and iii) meningiomas. Recently, authors experienced a case of Werner syndrome complicated by bone metastasis of rhabdomyosarcoma in a 20-year old Korean man. The patient revealed a painful mass on his right knee and progeroid features, short stature, scalp alopecia, abnormal dentition, craniofacial disproportion, hypothyroidsm, cataracts and osteoporosis. The onset of symptoms of Werner syndrome generally precedes any later symptoms of associated conditions, such as malignant tumor. Therefore, early recognition of Werner syndrome is important to assist identification of malignant tumors at an early stage in this patient group.
Fe-0.4C-2.3Si강의 기계적 성질에 미치는 오스템퍼링 열처리 조건의 영향
손제영 ( Je Young Son ),송준환 ( June Hwan Song ),김지훈 ( Ji Hun Kim ),예병준 ( Byung Joon Ye ) 한국주조공학회 2012 한국주조공학회지 Vol.32 No.2
The effect of heat treatment on mechanical properties of 0.4C-2.3Si(wt%) steel with bainitic ferrite matrix were investigated. This steel has been synthesized intergrating concepts from TRIP(Transformation Induced Plasticity) steel & Austempered Ductile Cast Iron(ADI) technology. The low alloy medium carbon (0.4 %C) steel with high silicon (2.3 %Si) was initially annealed for 60min at 800oC, 820oC and 840oC respectively in the intercritical region and then subsequently austempered at various temperatures at 260oC, 320oC and 380oC for 30 min in a salt bath. The mechanical properties were measured by using a tensile test. A detailed study of the microstructure of this steel after heat treatment was carried out by means of electron back scattering diffraction (EBSD) technic. In this study, a new low alloy steel with high strength (780~1,050MPa) and exceptionally high ductility (20~40%) was obtained.
입원한 소아에서 노로바이러스 급성 위장염의 임상 특성 및 유전형 분석 : 로타바이러스의 임상 특성과의 비교
송준환,선동신,박준수,최영진,남해선,김용배,정은혜,백경아,박귀성 대한감염학회 2010 감염과 화학요법 Vol.42 No.3
Background: Norovirus is one of the most prevalent pathogens causing acute gastroenteritis in children. We compared the clinical features of noroviral gastroenteritis to those of rotaviral gastroenteritis and analyzed the noroviruses' genotype frequencies. Materials and Methods: Stool samples were obtained form 433 children hospitalized with acute gastroenteritis from May 2008 through February 2009 at Soonchunhyang University Cheonan Hospital and examined for the presence of norovirus or rotavirus. We then analyzed the clinical features of noroviral gastroenteritis in comparison with rotaviral gastroenteritis and observed the capsid protein gene sequences from the isolated norovirus for genotyping. Results: Norovirus was isolated from 69 patients (16.4%) and rotavirus from 49 patients (11.6%). The noroviral gastroenteritis patients experienced vomiting (77.4%), diarrhea (73.2%), and respiratory symptoms (53.6%); the rotaviral gastroenteritis patients experienced diarrhea (71.4%), dehydration (69.3%), and vomiting (65.3%). Dehydration in patients with noroviral gastroenteritis (43.4%) was rare compared with rotavirus (69.3%) (P=0.008). The isolated norovirus belonged primarily to the GII.4 genogroup (85.5%). Our phylogenetic analysis of the GII.4 isolates revealed 3 clusters, including novel cluster C. Conclusions: Vomiting was the most common symptom in noroviral gastroenteritis patients. Dehydration in noroviral gastroenteritis patients was less common compared with rotavirus gastroenteritis patients. The majority of the norovirus strains isolated from children with acute gastroenteritis belonged to the GII.4 genogroup.