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서수홍,최병주,노치완,신채희,장성훈,김양수,어완규,김효경 고신대학교 의학부 2002 高神大學校 醫學部 論文集 Vol.17 No.1
The POEMS syndrome (polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, skin change) is a rare multisystemic disorder of unknown pathogenesis. Although the etiology is still unclear, proinflammatory cytokines such as tumor necrosis factor-α, IL-6. and paraprotein specificity for neuroendocrine tissue have been suggested to play a causative role. We report a case of POEMS syndrome presented as progressive sensorimotor neuropathy, hapatosplenomegaly, diabetes mellitus, solitary bone plasmacytoma, hypertrichosis and hyperpigmentation. The patient was treated with local irradiation and prednisolone and showed obvious neurological and systemic improvement.
서수홍,최병주,노치완,신채희,장성훈,김양수,어완규,김효경 고신대학교(의대) 고신대학교 의과대학 학술지 2002 고신대학교 의과대학 학술지 Vol.17 No.1
The POEMS syndrome (polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, skin change) is a rare multisystemic disroder of unknown pathogenesis. Although the etiology is still unclear, proinflammatory cytokines such as tumor necrosis factor-a, IL-6, and paraprotein specificity for neuroendocrine tissue have been suggested to play a causative role. We report a case of POEMS syndrome presented as progressive sensorimotor neuropathy, hepatosplenomegaly, diabetes mellitus, solitary bone plasmacytoma, hypertrichosis and hyperpigmentation. The patient was treated with local irradiation and prednisolone and showed obvious neurological and systemic improvement.