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박성춘(SC Park),황봉수(BS Whang),정성수(SS Chung),곽태로(TR Gwag) 대한산부인과학회 1985 Obstetrics & Gynecology Science Vol.28 No.8
The incidence of unilateral renal agenesis ascertained at autopsy of human beings averages between one in 600 and one in 1,200 In female the incidence of associated genital anomalies has been conservatively estimated as 50% In most women the genital anomaly consists of some degree of duplication of the uterus cervix and/or vagina and less commonly some form of partial atresia . Embriologically the mullerian ducts develop just lateral to the mesonephric ducts which have been postulated to act as a guide to the growth of the mullerian duct Because the urinary and genital systems are derived from a common embryonic mesoderm it is easy to imagine an early teratogenic influence leading to simultaneous defects in both systems The mesonephric duct abnormality appears responsible for the lack of a normal ureteric dud which results in later renal agenesis The renal agenesis is predominant in the right side but it is not clear why there appears to be a right-sided predominance Uterus didelphys is more commonly observed although a bicornuate or septate uterus is documented in a few instances Recently we have had 3 cases of septate uterus is documented in a few instances agenesis at the Wallace Memorial Baptist Hospital of which one was uterus didelphys and the others were bicornuate uterus and septate uterus.
정성수(SS Chung),박성춘(SC Park),황봉수(BS Whang),제구화(KW Je) 대한산부인과학회 1985 Obstetrics & Gynecology Science Vol.28 No.11
Thanatophoric dwarfism is a lethal congenital chondrodystrophy characterized by diminished vertebral body height a narrowed throax and micromellia The diagnosis is confirmed by clinical features radiological and histological findings Recently we have experienced a case of thanatophoric dwarfism and reviewed it briefly.
황봉수(BS Whang),박성춘(SC Park),유금준(GJ Yoo),이강국(KK Lee) 대한산부인과학회 1986 Obstetrics & Gynecology Science Vol.29 No.2
Chorioangioma is a common primary benign tumor of the placenta, and the incidence of chorioangioma is higher than generally realized that because of poor routine histologic examination of the placenta. Hydramnios and premature delivery are commonly found when large chorioangioma is combined. We have had an experience of a case of chorioangioma with hydramnios, premature rupture of membrane, and premature delivery in 27 years old multigravida. Now we report the case and review with literatures briefly.
권해석(HS Kuen),박성춘(SC Park),김중근(JG Kim),곽태로(TR Gwag),백옥기(OK Paik) 대한산부인과학회 1985 Obstetrics & Gynecology Science Vol.28 No.6
Cloacal exstrophy is a rare congenital marformation and a distinctive morphologic syndrome. The cardinal clinical features of cloacal exstrohy consist of exstrophy of the bladder, omphalocele, prolapse of the intestine, imperforate anus and lumbosacral myelocele. The essential feature of the syndrome is a failure of cloacal separation at 4~5 weeks of gestation, which results in a persistent cloaca into which the ureter and a rudimentary hindgut open. Most cases of cloacal exstrophy are sporadic, and none has been shown to be genetic in origin. Surgical treatment has been carried with limited effectiveness. The prognosis may be hopeless in a significant number of these infant. Recently we have experienced a case of exstrophy of cloaca in Korea for the first time and we are to report it with brief review of literature.