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김명주 ( Myoung Joo Kim ),김성현 ( Seong Hyun Kim ),최혜영 ( Hae Young Choi ),명기범 ( Ki Bum Myung ),최유원 ( You Won Choi ) 대한피부과학회 2006 대한피부과학회지 Vol.44 No.6
Spindle cell hemangioendothelioma was first described in 1986 to characterize a particular angiomatous lesion which shows different clinical features, however, it has recently been designated as spindle cell hemangioma (SCH) due to its benign nature. Microscopically, this peculiar vascular tumor consists of cavernous blood vessels intermixed with solid areas predominantly composed of spindle cells, resembling Kaposi sarcoma. A 39-year-old woman presented with a bean-sized, tender, bluish nodule on the pulp of her right thumb. The 1 year old lesion had increased slowly in size over this time. Histologic examination of the lesion showed that it was composed of large irregularly-dilated, thin-walled cavernous blood spaces containing organizing thrombi, numerous red blood cells, and a spindle cell mass which was partially connected with the vessel wall and invaded the stroma. A diagnosis of SCH was made based on histologic and immunohistochemical findings. After the lesion was totally excised, there has been neither recurrence nor occurence of new lesions to date. (Korean J Dermatol 2006;44(6):741~744)
비전형적인 조직 소견을 보이는 후천성 반응성 천공성 교원증 1 예
김성현(Seong Hyun Kim),신정현(Jeoung Hyun Shin),최혜영(Hae Young Choi),명기범(Ki Bum Myoung) 대한피부과학회 2001 대한피부과학회지 Vol.39 No.10
Reactive perforating collagenosis(RPC) is a kind of perforating dermatosis characterized by transepidermal elimination of altered dermal collagen. RPC is classified into two forms; childhood or inherited form, and adulthood or acquired form. Acquired RPC is reported to occur in association with the severe complicated diabetes mellitus, chronic renal failure and other diseases. We describe a 43-year-old Korean woman with atypical acquired RPC associated with uncontrolled diabetes mellitus and severe pruritus. The histopathologic findings of the lesions showed neither transepidermal channel nor cup-shaped epidermal depression. Multiple degenerated collagen bundles arranged vertically and were eliminated through epidermis to the surface individually. Transmission electron microscopic findings showed the same as typical RPC. Skin lesions improved after the insulin subcutaneous injections, UVB phototherapy & antihistamine administration. (Korean J Dermatol 2001;39(10): 1133-1137)
김문정,장가연,임연순,최혜영,명기범 梨花女子大學校 醫科大學 醫科學硏究所 1999 EMJ (Ewha medical journal) Vol.22 No.1
Granular cell tumor(GCT) is an uncommon tumor characterized clinically by an asympto-matic, solitary nodule in the tongue and skin, especially head and neck region. Histopa-thologically the broad fascicles of tumor cells infiltrate the dermis and the tumor cells are characterized by plump cells with faint eosinophilic, granular cytoplasm. The origin of cells has been debated for decades. However electron microscopic and imm-unohistochemical studies strongly support a Schwann cell origin. We report a case of granular cell tumor arising from the anterior chest of 12-year-old healthy girl, which exhibited the distinctive histopathologic appearance and also reactive with PAS, S-100, and NSE.