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종양연관성 성조숙과 과도신체발육을 동반한 소아 간암 -2예 보고-
김옥화 대한영상의학회 1990 대한영상의학회지 Vol.26 No.2
Sexual precocity in a 28-months-old boy and markedly accelerated skeletal growth with large body in a 5 years and 5 months-old-girl are reported. The former resulted from human chorionic gonadotropin-producing hapatoblastoma and the latter from cerebral gigantism associated with hepatoma, These two different disorders are discussed on the common basis of rare association of malignant hepatic tumors with precocious sexual and/or somatic growth. The clinical manifestations, chemical abnormalities, and the radiologic findings are presented with a brief review of the literature.
Desmoplastic Fibroma of Bone in a Toe: Radiographic and MRI Findings
김옥화,김선정,김지연,류지화,추혜정,이선주,이인숙,서경진 대한영상의학회 2013 Korean Journal of Radiology Vol.14 No.6
Desmoplastic fibroma is a rare benign primary bone tumor that is histologically similar to the soft tissue desmoid tumor. It most often involves the mandible, large long bone or iliac bone. Desmoplastic fibroma in a toe has been extremely rarely reported. Authors report a rare case of desmoplastic fibroma of bone occurring in the distal phalanx of a foot, with descriptions of the radiographic and MRI findings, correlation of the radiologic and pathologic findings, and discussion on the differential diagnosis of the tumor.
김옥화 대한영상의학회 2015 대한영상의학회지 Vol.72 No.3
Hemangioblastoma is a benign vascular neoplasm of the central nervous system that occurs frequently in the cerebellum and other areas of the central nervous system including spinal cord and brainstem. Spinal hemangioblastoma can present as a sporadic isolated lesion or as a component of von Hippel-Lindau syndrome. The author presents a case of 32-year-old man with von Hippel-Lindau syndrome and spinal hemangioblastomas represented by multiple small spinal lesions, with an emphasis on the magnetic resonance imaging findings and clinical characteristics of von Hippel-Lindau syndrome-associated spinal hemangioblastomas.
Spinal Meningeal Melanocytoma with Benign Histology Showing Leptomeningeal Spread: Case Report
김옥화,김선정,추혜정,이선주,이인숙,김지연,김훈 대한영상의학회 2013 Korean Journal of Radiology Vol.14 No.3
Meningeal melanocytoma is a rare benign tumor with relatively good prognosis. However, local aggressive behavior of meningeal melanocytoma has been reported, especially in cases of incomplete surgical resection. Malignant transformation was raised as possible cause by prior reports to explain this phenomenon. We present an unusual case of meningeal melanocytoma associated with histologically benign leptomeningeal spread and its subsequent aggressive clinical course, and describe its radiological findings.
Radiologic Features of Proteus Syndrome: A Case Report
김옥화 대한영상의학회 2014 대한영상의학회지 Vol.70 No.4
Proteus syndrome is a rare congenital hamartomatous condition that is characterized by a wide range of malformations with overgrowth of various tissues. The author reports the case of a Proteus syndrome in a 14-year-old girl who had the unique features of this syndrome including megaspondylodysplasia with resultant scoliosis, leg discrepancy, macrodactyly, clinodactyly, hyperostosis in external auditory meatus, asymmetric megalencephaly, splenomegaly, cystic lung changes, asymmetric soft tissue fat infiltrations and a long, asymmetric face, with descriptions of the radiological features.
Extraskeletal Chondroma Causing Carpal Tunnel Syndrome: A Case Report
김옥화,김연미 대한영상의학회 2014 대한영상의학회지 Vol.70 No.3
Carpal tunnel syndrome caused by extraskeletal chondroma has been scarcely reported in the literature. Authors report a case of carpal tunnel syndrome as a result of an extraskeletal chondroma arising within the carpal tunnel, and describe the radiological and pathological findings of the mass. We also discuss the differential diagnosis of the calcified space, occupying lesions that may occur in carpal tunnel.
출생시 체중 1500 그램 미만의 심한 저체중 미숙아들의 흉부질환
김옥화 대한영상의학회 1990 대한영상의학회지 Vol.26 No.2
Since the introduction of the intensive perinatal care, the surviral rate of the infants weighing less than 1500 gm at birth has improved substantially. However, pulmonary diseases remain to be the major causes of the high mortality of these low birthweight infants. In order to systematically assess an epidmiologic distribution of the pulmonary diseases in these very low weight prematures, we have analyzed the chest x-rays of 102 infants weighing less than 1500gm. These consisted of 30 with extreme low birth weight (ELBW) weighing less than 1000gm and 72 with very low birth weight (VLBW) weighing 1001-1500gm. The survival rate of ELBW and VLBW was 10% and 49%, respectively. Seventy of 102 infants had abnormal findings in the chest x-ray. Forty-eight had idiopathic respiratory distress syndrome (IRDS), 8 immature lung, 6 Wilson-Mikity syndrome, 4 pneumonia, 2 pulmonary hemorrhage, 1 congenital heart disease, and 1 suspicious Pierre-Robin syndrome. seven out of 48 infants with I DS had persistent ductus arteriosus and in only 2(30%) of 7 cases were alive. Endotracheal intubation and assisted ventilation application for the treatment of IRDS resulted in pulmonary interstitial emphysema in 4 infants and pneumothorax and/or pneumomediastinum in 4 infants. Displacement of endotracheal intubation showed lobar and/or unilateral lung atelectasis in 8 infants and a case of accidental dislodgement of intubation tube into the esophagus resulted in air esophagogram and worsened lung aeration. In spite of the development of many sophisticated methods of diagnostic radiology, the chest x-ray was still the most valuable yet simple way of evaluating the pulmonary problems in these extreme and very low birth weight prematures.
김옥화 인제대학교 백병원 2003 仁濟醫學 Vol.24 No.1
Xanthogranulomatous inflammation is an unusual form of chronic inflammation that may make masslike lesion to simulate malignancy radiologically. To knowledge, xanthogranulomatous inflammation in the urachal remnant has not been previously reported. I describe clinical. pathological and radiological findings of a rare xanthogranulomatous inflammation occuring in the urachal remnant.