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김순남(Soon Nam Kim),차병호(Byung Ho Cha),이준수(Joon Soo Lee),고창준(Chang Jun Coe) 대한소아신경학회 1995 대한소아신경학회지 Vol.2 No.2
59 cases with partial agenesis of corpus callosum visited to Department of pediatrics. College of medicine, Yonsei university, from Jan.1980 to Dec.1993, were reviewed on the basis of clinical characteristics. The results were summarized as follows: the age distribution were 31 cases(52.5%) under 1year, 20 cases(33.8%) from 1 to 5 years, 8 cases(13.7%) from 6 to 15 years. Sex distribution revealed males to females to be 1:1.2. All cases shewed mental retardation, 30 cases(50.8%) with seizure, 8 cases(13.6%) with cerebral palsy, and the most common type of seizure was generalized tonic clonic seizure. 24 of 56 patients had abnormal perinatal history: 22% of them had perinatal asphyxia, 10%. low birth weight, 6.7%. prematurity. 48 patients had associated anomalies. among which craniofacial anomaly was the most common and 8 patients had cardiovascular. 8 patients, skeletal anomalies. We used Griffith developmental scale to assess the developmental status in 31 cases. None of the cases achieved the score above 85 for general intelligence quotient and 24 cases were below 55. EEG revealed most commonly asymmetricity between two hemispheres. some of them showed spikes and slow waves.
김순남(Soon Nam Kim),이준수(Joon Soo Lee),차병호(Byung Ho Cha),고창준(Chang Jun Coe) 대한소아신경학회 1995 대한소아신경학회지 Vol.3 No.1
Batten disease (Neuronal ceroid lipofuscinosis, NCL) is the term describing a group of neurodegenerative diseases of which the major pathognomonic feature is the accumulation of autofluorescent lipopigment in various tissues including neurons. This study presents the clinical features of 6 patients who had been diagnosed as Batten disease by means of skin biopsy and electron microscopic evaluation from March. 1989 to March 1994.
Haemophilus influenzae Type b 에 대한 급성 후두염의 치료 경험 2 례
이수영(Soo Young Lee),유상호(Sang Ho Yoo),이기선(Ki Sun Lee),홍미애(Mi Ae Hong),김순남(Soon Nam Kim) 대한소아알레르기호흡기학회 1998 소아알레르기 및 호흡기학회지 Vol.8 No.1
Epiglottitis is an uncommon but potentially life threatening infectious disease in young children. And it is rapidly progressing cellulitis of the epiglottis and adjacent structures that has the potential for causing abrupt, complete airway obstruction. The most common cause of acute epiglottitis is Haemophilius influenzae type b (Hib), therefore in USA, the acute epiglottitis is seen less commonly since the wide spread use of immunization against Hib. In Korea, there has been no report of acute epiglottitis caused by known bacterial organism, and a little investigation of the effects of the immunization against Hib, or Hib related respiratory diseases. In this report, we describe two cases of acute epiglottitis caused by Hib, occurred in non-immunized young-male children admitted to Ajou University Hospital. They had visited to the emergency center of Ajou University hospital with the complaints of acute fever, drooling, dysphagia and severe respiratory difficulties. In both cases, we observed the cherry-red colored, severely swollen epiglottis by the direct laryngoscopic examination. Hib was cultured in blood samples from both two cases, and the patients treated successfully by the 3 days of endotracheal intubation and proper antibiotics therapy without any complications such as pneumonia, meningitis, osteomyelitis, or pericarditis.
Establishment of the National Standard for Prekallikrein Activator with a Collaborative Study
In Soo Shin(신인수),Jae Yeon Cho(조재연),Soon Nam Kim(김순남),Choong Man Hong(홍충만),Ki Hong Lee(이기홍),Ho Jung Oh(오호정),Si Hyung Yoo(유시형),Jae Hyun Lim(임재현),Seung Eun Choi(최승은),Colin Longstaff,Hong Ki Min(민홍기),Sue 한국생물공학회 2004 한국생물공학회 학술대회 Vol.2004 No.4
근무력증과 왜소증을 동반한 Bartter syndrome 1례
김인성,강주형,신윤혜,이동국,김순남,배기수,Kim In-Sung,Kang Ju-Hyung,Shin Yun-Hei,Lee Dong-Kuk,Kim Soon-Nam,Pai Ki-Soo 대한소아신장학회 2002 Childhood kidney diseases Vol.6 No.2
저자들은 본원 소아과에 입원한 9년 3개월된 남아에서 만성병색소견, 심한 근무력증, 왜소증, 저칼륨성 대사성 알칼리혈증 및 신석회증과 좌측 요관의 확장을 보이는 영아기 이후 발병한 Bartter 증후군 1례를 경험하였기에 치료반응 및 임상경과를 문헌 고찰과 함께 보고하는 바이다. Bartter syndrome is a rare disorder characterized by the association of hypokalemic hypochloremic metabolic alkalosis, hyperreninemia, hyperaldosteronemia, short stature and nephrocalcinosis. This disorder presents with hyperplasia of juxtaglomerular apparatus on renal biopsy. We experienced a case of late-onset Bartter syndrome with nephrocalcinosis in a 9-year-old boy, whose chief pictures were muscle weakness, short stature, persistent sterile pyuria and microscopic hematuria. We report this case with a brief review of related literatures.