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Prednisolone과 Interferon alfa - 2a로 치료하여 호전된 미만성 신생아 혈관종증
조흔정 ( Heun Jung Cho ),김동건 ( Dong Kun Kim ),박경득 ( Kyung Deuk Park ),양창현 ( Chang Hyun Yang ),이진용 ( Jin Yong Lee ),김길영 ( Kir Young Kim ) 대한피부과학회 1996 대한피부과학회지 Vol.34 No.6
Diffuse neonatal hemangiomatosis is a disease often with a fatal out,come, characterized by widespread capillary hemangiomias of the skin and visceral organs. A 6 month old-girl was diagnosed to have diffuse neonatal hemangiomatosis by her multiple hemangiomas on the skin, liver, brain, lung and oral mucosa. She was treated with prednisolone 1.5-2rng/kg/day for 9 months and combined interferon alfa-2a 3 million unit/m2/day for 5months. During the treatment the number and size of hemangio~rnas were markedly r'duced. (Kor J Dermatol 1996;34(6): 1039-1043)
重症 再生不良性貧血에 있어서 骨髓移植 및 抗 T-임파球글로불린療法의 臨床的 效果
金吉英 연세대학교 대학원 1985 延世論叢 Vol.21 No.5
Nine patients with severe aplastic anemia were treated with bone marrow transplantation with and without anti-human thymocyte globulin (ATG, ATGAMR) between April 1981 and August 1984. Two patients who received Isogeneic or Syngeneic bone marrow transplantation had hematologic recovery within 4 weeks after marrow transplantation. Another two patients received Allogeneic bone marrow transplantation and only one had evidence of engraftment. Another three patients were treated with horse anti-human thymocyte globulin. Two out of three had complete and minimal response by defined criteria respectively. The remaining one patient did not respond. Two of nine patients received an infusion of HLA-haploidentical marrow ceils after ATG administration and both had partial responses-improvement in all three cell lines, absence of infections and no transfusion requirement. Six patients (77. 8%) are surviving between 6 and 46 months. and two have died. Deaths were due to systemic infection and/or peptic shock. Data from this stuffy suggest that results of marrow transplantation are beat for those patients with HLA-compatible identical twin donors. However, for severe aplastic anemia with HLA-haploidentical donors, marrow infusion with ATG therapy were also potentially important therapeutic regimens.