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성인 황색육아종의 임상, 병리조직 및 면역조직화학적 연구
곽현빈 ( Hyun-bin Kwak ),정의성 ( Eui Sung Jung ),박상우 ( Sang-woo Park ),윤석권 ( Seok-kweon Yun ) 대한피부과학회 2019 大韓皮膚科學會誌 Vol.57 No.5
Background: Juvenile xanthogranuloma is a benign, self-limited disorder that usually occurs in infants and young children. Xanthogranuloma is rare in adults, and therefore studies reporting adult xanthogranuloma are limited. Objective: We investigated the clinical, histopathological, and immunohistochemical characteristics of adult xanthogranuloma. Methods: In this study, we evaluated 20 lesions in 19 patients with adult xanthogranuloma. Results: A male predominance was observed (male:female ratio 1.4:1), and the mean age of patients was 35.1±16.3 years (range 15∼66 years), with the peak incidence observed in patients in their 20s. Notably, 65.0% of the lesions developed on the head and neck. The nodular form was more common than the papular form of this condition. Histopathological examination revealed dense monomorphic histiocytic infiltration without lipidization and scattered eosinophils without multinuclear giant cells in 5 lesions (25.0%), foamy histiocytic infiltration with variations of completely developed Touton giant cells in 10 lesions (50.0%), and fibrohistiocytic proliferation in 3 lesions (15.0%). On immunohistochemical examination, histiocytes including giant cells showed positive test results with Factor XIIIa (90.9%), vimentin (100%), and CD68 (100%) and negative test results with CD1a, smooth muscle actin, and S-100 protein stains. Tumor excision was the treatment for choice. Conclusion: Adult xanthogranuloma most commonly manifested as the nodular form of the disease on the head and neck of men in their late 20s. Histopathologically, the classic Touton cell-rich stage was most commonly observed, followed by the stage of early predominantly mononuclear infiltration. This was a single-center, small-sized retrospective study; however, we expect the results of this study to contribute to a better understanding of adult xanthogranuloma. (Korean J Dermatol 2019;57(5):243∼250)
박상우 ( Sang-woo Park ),곽현빈 ( Hyun-bin Kwak ),정의성 ( Eui-sung Jung ),유효현 ( Hyo-hyun Yoo ),남경화 ( Kyung-hwa Nam ),박진 ( Jin Park ),김한욱 ( Han-uk Kim ),윤석권 ( Seok-kweon Yun ) 대한피부과학회 2019 大韓皮膚科學會誌 Vol.57 No.4
Amputation of the lower extremities followed by the use of an artificial leg is very common. However, malignancy arising in an amputation stump is an extremely rare event. In this report, we describe a case of squamous cell carcinoma arising in the amputation stump of a 56-year-old Korean man. To the best of our knowledge, similar cases have not been previously reported in Korea. (Korean J Dermatol 2019;57(4):191∼193)
우수한 ( Soo-han Woo ),곽현빈 ( Hyun-bin Kwak ),박수경 ( Su-kyung Park ),박진 ( Jin Park ),윤석권 ( Seok-kweon Yun ),김한욱 ( Han-uk Kim ) 대한피부과학회 2017 大韓皮膚科學會誌 Vol.55 No.10
Angiomyxolipoma is a recently described and rare variant of lipoma that is characterized by the proliferation of adipose tissue with a myxoid stroma and multiple thick and thin-walled blood vessels. A 51-year-old man presented with a tender subcutaneous nodule on his right arm. The tumor was completely removed by excisional biopsy, and the histopathologic features revealed a thin fibrous capsule with incomplete fibrous septa extending into the lesion, dividing it into lobules of different sizes. The fat cells were mature, with a single vacuole and an eccentric nucleus. The vascular component consisted of groups of capillaries and occasional vessels of larger caliber. Erythrocytes were present within the lumen, and myxoid stroma was found. He was diagnosed as having angiomyxolipoma. Herein, we report a rare case of subcutaneous angiomyxolipoma of the arm. We also review and discuss such cases in the literature. (Korean J Dermatol 2017;55(10):680∼683)