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양측의 비폐쇄성 수신증과 요관 확장이 동반된 선천성 신성요붕증
장영이 ( Yung Yi Chang ),김형욱 ( Hyung Uk Kim ),김형두 ( Hyung Du Kim ),신영신 ( Shin Young Shin ),이종민 ( Jong Min Lee ),김혜수 ( Hae Su Kim ),김석영 ( Suk Kyung Kim ),방병기 ( Byung Ki Bang ) 대한신장학회 2002 Kidney Research and Clinical Practice Vol.21 No.6
We describe a case of congenital nephrogenic diabetes insipidus with severe dilatation of bilateral urinary tracts without anatomical obstructions. Functional obstruction can be occurred when polyuria surpasses the transporting ability of urine in the urinary tract. The patient was admitted to our hospital due to decreased mentality developed after traffic accident. On radiologic study, bilateral hydronephrosis and hydroureter were noted. Because the patient excreted copious dilute urine, we performed water deprivation test and the result was consistent with nephrogenic diabetes insipidus. We are presenting this case in an attempt to describe strong association between congenital diabetes insipidus and nonobstructive hydronephrosis in which polyuria is responsible for the hydronephrosis.