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서종근 ( Jong Keun Seo ),강주현 ( Ju Hyun Kang ),조경종 ( Kyung Jong Cho ),이드보라 ( Deborah Lee ),황선욱 ( Seon Wook Hwang ),성호석 ( Ho Suk Sung ) 대한피부과학회 2009 대한피부과학회지 Vol.47 No.2
Reactive perforating collagenosis (RPC) is one of a range of essential perforating disorders. Two types have been recognized: the childhood or inherited form, and the adult or acquired form. Acquired RPC is usually associated with systemic diseases, especially diabetes mellitus, and/or renal failure. We present a case of a 47-year-old female with umbilicated skin lesions triggered by an insect bite. Histology from the lesion revealed transepidermal elimination of collagen. (Korean J Dermatol 2009;47(2):196∼198)
지속성 발진성 반상 모세혈관 확장증의 임상 및 병리조직학적 고찰
이드보라 ( Deborah Lee ),조경종 ( Kyung Jong Cho ),김정욱 ( Jung Wook Kim ),강미선 ( Mi Seon Kang ),성호석 ( Ho Suk Sung ),황선욱 ( Seon Wook Hwang ) 대한피부과학회 2008 대한피부과학회지 Vol.46 No.10
Background: Telangiectasia macularis eruptiva perstans (TMEP) is a rare form of cutaneous mastocytosis, and this is characterized by multiple brownish-red confluent macules and telangiectasia. Although several cases of TMEP have been reported in the Korean literature, no clinicopathological studies have yet been reported. Objective: This study was undertaken to document the clinical features of TMEP, to examine the histopathological features of TMEP and to quantify the number of perivascular mast cell by using the `mast cells per vessel unit` method (MPV). Methods: The medical records of 16 patients with TMEP and who were seen at our institution from 1999 through 2006 were retrieved. We retrospectively reviewed the medical records, clinical photographs and histopathology slides of these patients. Furthermore, we quantified the number of perivascular mast cells, using the MPV method, on the slides of the TMEP patients, and then we compared this to the number of perivascular mast cells in normal skin (n=10) and urticaria pigmentosa skin (UP, n=10) as controls. Results: The ratio of male to female was 13:3 and the mean age of onset was 36.31±12.34 years. The most commonly involved sites were both the trunk and upper extremities (62.5%). 5 patients (31.3%) showed constitutional symptoms. A microscopic examination demonstrated scant perivascular infiltrate with mast cells. The average number of mast cells less than 55μm of vessel diameter in the TMEP, normal skin and UP was 3.32, 1.17 and 5.89, respectively and the average number of mast cells that were more than 55μm in the TMEP, normal skin and UP was 7.00, 2.08 and 21.00, respectively and these values showed statistical differences (p<.0001). The MPV that was of less than 55μm of vessel diameter in the patients with associated cutaneous or systemic symptoms was greater that that of the patients without associated symptoms and these values showed statistical differences (p<.005). Conclusion: This study suggested that TMEP can be associated various constitutional and cutaneous symptoms. The MPV method can be an effective method for differentiating the histopathologic findings of TMEP from those of normal skin or UP. (Korean J Dermatol 2008;46(10):1303∼1308)
피부 이완의 소견을 보인 상염색체 열성 2형 탄력섬유 가성황색종
황선욱 ( Seon Wook Hwang ),조경종 ( Kyung Jong Cho ),오두진 ( Doo Jin Oh ),이드보라 ( Deborah Lee ),김정욱 ( Jung Wook Kim ),박성욱 ( Sung Wook Park ) 대한피부과학회 2007 대한피부과학회지 Vol.45 No.10
Pseudoxanthoma elasticum is a rare, heritable disorder of elastic fibers characterized by yellowish, coalescing papules on the loose and wrinkled flexural skin. An 18-year-old man presented cutis laxa-like marked wrinkling on the axillae, trunk and thighs for about 10 years. There was no similar skin lesion on his family members and no other systemic involvement was found. Histopathological examination of the abdomen revealed fragmentation and calcification of elastic fibers in the middle and lower dermis. Von Kossa staining showed calcium deposition along the altered elastic fibers. Herein, we report a rare case of autosomal recessive pseudoxanthoma elasticum presenting generalized cutaneous laxity. (Korean J Dermatol 2007;45(10):1083∼1086)
황선욱 ( Seon Wook Hwang ),조경종 ( Kyung Jong Cho ),홍순권 ( Soon Kwon Hong ),서종근 ( Jong Keun Seo ),이드보라 ( Deborah Lee ),성호석 ( Ho Suk Sung ) 대한피부과학회 2008 대한피부과학회지 Vol.46 No.6
Accumulation of calcium in the skin is usually classified as a group of disorders referred to as calcinosis cutis. Based on pathophysiologic mechanisms, it has been classified as metastatic, dystrophic, idiopathinic and iatrogenic calcinosis cutis. Local tissue injury due to repetitive trauma by an acupuncture needle can cause dystrophic calcinosis cutis. A 61-year-old woman developed hyperpigmented pea sized subcutaneous nodules on the right side of her lower abdomen. She had received several sessions of acupuncture treatments on the right abdomen in a herb medicine clinic. A biopsy specimen showed amorphous basophilic deposits in the dermis and serum levels of calcium, phosphate were within the normal range. We report a case of dystrophic calcinosis cutis following acupuncture treatments by a herb medicine doctor. (Korean J Dermatol 2008;46(6):839∼841)
황선욱 ( Seon Wook Hwang ),조경종 ( Kyung Jong Cho ),오두진 ( Doo Jin Oh ),이드보라 ( Deborah Lee ),김정욱 ( Jung Wook Kim ),박성욱 ( Sung Wook Park ) 대한피부과학회 2006 大韓皮膚科學會誌 Vol.44 No.12
A 17-year-old woman was stung by a jellyfish on her right lower leg in waters off the Korean coastline. The lesions presented as erythematous, painful patches and cleared-up within 2 weeks. However, 2 weeks later, erythematous band-like patches and crusts developed at the previous contact site and similar lesions occurred on non-contact areas. Histologic examination revealed hyperkeratosis, focal spongiosis in the epidermis and perivascular lymphohistiocytic infiltrate, with numerous eosinophils in the upper dermis. We report a case of jellyfish dermatitis which showed immediate toxic reaction and delayed cutaneous reaction following a jellyfish sting from a species present in Korea. (Korean J Dermatol 2006;44(12):1451~1453)
IPL 치료 후 발생한 Intravascular Papillary Endothelial Hyperplasia
황선욱 ( Seon Wook Hwang ),조경종 ( Kyung Jong Cho ),강주현 ( Ju Hyun Kang ),이드보라 ( Deborah Lee ),김정욱 ( Jung Wook Kim ),박성욱 ( Sung Wook Park ) 대한피부과학회 2008 대한피부과학회지 Vol.46 No.2
Intravascular papillary endothelial hyperplasia (IPEH) is a rare benign vascular tumor characterized by the development of endothelial-lined papillary projections in the vascular lumen. Most authors believe that IPEH represents an unusual pattern of organizing thrombus, implying that a thrombus is the initial cause. A 13-year-old boy came to hospital because of a purpuric patch and violaceous plaque on his right forearm. Clinically, the lesions were thought to be a hemangioma or other vascular malformation. Therefore, we treated him with intense pulsed light (IPL) four times. After treatment, the initial skin lesions were erythematous and edematous and a new bluish mass and multiple scattered subcutaneous nodules appeared near the original skin lesions. Histologic examination of the new bluish mass showed an organic thrombus and endothelial-lined capillary projections in the dilated vascular lumen, compatible with IPEH. Here, we report an interesting case of IPEH after IPL treatment in a 13 year-old boy. (Korean J Dermatol 2008;46(2):234∼237)
전신성 홍반성 루프스와 이차성 항인지질 항체 증후군 환자에서 발생한 망상 청피반
김정욱 ( Jung Wook Kim ),오두진 ( Doo Jin Oh ),조경종 ( Kyung Jong Cho ),홍순권 ( Soon Kwon Hong ),이드보라 ( De Bo Rah Lee ),황선욱 ( Seon Wook Hwang ),박성욱 ( Sung Wook Park ) 대한피부과학회 2007 대한피부과학회지 Vol.45 No.6
Antiphospholipid syndrome is defined as the presence of lupus anticoagulant antibodies or anticardiolipin antibodies with vascular thrombosis or specific pregnancy complications. Antiphospholipid syndrome can be associated with autoimmune, malignant or infectious diseases. Cutaneous manifestations of antiphospholipid syndrome are variable and can be a first clue to the syndrome or other associated diseases. We report a case of systemic lupus erythematosus and secondary antiphospholipid syndrome presenting as livedo reticularis on both legs of a patient. We recommend that patients with livedo reticularis should be examined for systemic lupus erythematosus or antiphospholipid syndrome. (Korean J Dermatol 2007;45(6):622∼625)