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PUVA 요법으로 현저한 호전을 보인 지속성 발진성 반상 모세혈관확장증
성순제,백영곤,유희준,손숙자 ( Sun Je Sung,Young Gon Baik,Hee Joon Yu,Sook Ja Son ) 대한피부과학회 1991 대한피부과학회지 Vol.29 No.5
Telangiectasia macularis eruptiva perstans(TEMP) is an unusual type of urticaria pigmentosa, the eruption of which usually occurs in adults and consists of red telangiectatic macules. The lesions tend to be very persistent and unresponsive to treatment. We report a case of TEMP occurred in a 26 year-old woman. The patient had numerous pea sized reddish brown telangiectatic macules with positive Darier`s sign on the trunk and extermities for 7 years. Histopathologic findings were remarkable for numerous mast cells and telangiectasia on the upper dermis. With a trial of PUVA therapy(total 215J/㎠), the skin lesions almost completely resolved.
급성 두창양 태선양 비강진의 임상적 및 병리조직학적 관찰
성순제(Sun Je Sung),유희준(Hee Joon Yu),손숙자(Sook Ja Son) 대한피부과학회 1991 대한피부과학회지 Vol.29 No.3
We reviewed the clinical features and the skin biopsy slides of 27 patients who were diagnosed as PLEVA clinically or histapathologically in order to evaluate the clinical characteristics and the specific histopathological findings of PLEVA. The results were as follows : l. 13 of these 27 cases(48%) were confirmed as PLEVA. 2. PLEVA was more frequent in males(85% ), most of whom were young adults. 3. In most cases of PLEVA, the predilection site was on the trunk and extremities, and mild pruritus was a characteristic complaint. 4. Most cases of PLEVA were treated with tetracycline or PUVA therapy with temporary remission, but this therapy did not decrease the rate of recurrence. 5. Some histopathological findings previously described as typical in PLEVA(eg, trapped RBC in the epidermis, exocytosis of lymphocyte, dermal hernorrhage and lymphocytic perivasculitis) seemed not to be specific and were often seen in a variety of other dermatoses. 6. The histopathological findings of linear parakeratosis(85%) and dyskeratotic cells in the middle and upper epidermis(92% ) seemed to be significant findings for PLEUA. 7. The above mentioned histopat,hological findings for PLEVA were frequently found from the vesicular lesions or necrotic hemorrhagic papules. (Kor J Dermatal 20(3): 348 353,1001)