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姜致重,柳在雲 최신의학사 1974 最新醫學 Vol.17 No.9
A pedigree investigation was made on a family with five cases of Osteogenesis Imperpecta. Clinical and radiological features were examined in 3 of the cases. Most of the cases examined, belong to Osteogenesis Imperpecta Tarda, and the mode of inheritance seems to be autosomal dominant form.
姜致重 順天鄕大學校 1974 의대논문집 Vol.1 No.-
A histometrical study of 46 spleen, of which 20 normal and 26 splenomegalic, were done. It shows : 1. a) Thc volume of splenic #sinus and area of the sinus cord junction is larger in splenomegalic than in normal spleen. b) The mean seetional area of splenic sinus is same in both normal and pathologic. c) The mean diameter of splenic cord is smaller in splenomegalic than in normal spleen. 2. The size of splenic sinus is same in both # splenomegalic and normal one in every measurement. 3. Accordingly, no significant correlationship was found in the mean area of seetion of splenic sinus, volume of the splenic sinus and the mean diameter of the splenic cord between normal and splenomegalic spleen. However, there were significant correlationship of plus or minus in the other 8 measurements between normal and splenomegalic spleens. 4. The process of making up of the splenomegaly # in portal hypertension could be thus estimated as follows : In portal hypertension, the increased pressure in sinuses result division of Maschengangsmantel into multiple small sinuses and consequent channclling between end arteries and sinuses. This brings decrease of the # resistance of the blood stream and increase of # arterial vaseularization. These result the increase in number of end arteries and consequent # building of new splenic cords. These new splenic cords are divided again into multiple small # new sinuses and repeat the above mentioned process. These repeated process reslut splenomegaly.