소뇌교각에 발생된 원발성 황문근육종 1예 = A Case of Primary Rhabdomyosarcoma in the Left Cerebello-Pontine Angle

다국어 초록 (Multilingual Abstract)

The primary rhabdomyosarcoma of the brain is very rare. There are only 14 cases reported in the literatures till 1975, and the majority of them were arised in the cerebellum.
The intracranial rhabdomyosarcomas may be originated from the multipotent mesenchymal cells of aberren?? muscle tissue in the leptomeninges.
The histological 3 types are adult pleomorphic, alveolar and embryonal type. The demonstration of cross-striation is confirmed for diagnosis of this tumor.
All of these tumors tend to have a short clinical course, but the survival time seems to be slightly improved by surgical excision followed by radiotherapy.
We have recently experienced one case of primary rhabdomyosarcoma in the left cerebello-pontine angle of 9 year-old girl, which was confirmed by operation and complete autopsy.