산전 진단된 선천성 낭성 선종양 폐기형 1 예 = A Case of Antenatally Diagnosed Cystic Adenomatoid Malformation of Lung

국문 초록 (Abstract)

본 저자들은 임신 24주+5일에 시행한 산전 초음파검사상 선천성 낭포성 유선종 폐기형을 의심하여 임공 임신 중절 후 병리학적으로 확진된(type Ⅱ & Ⅲ, mixed) 1예를 경험하였기에 간단한 문헌적 고찰과 함께 보고하는 바이다.

다국어 초록 (Multilingual Abstract)

Congenital cystic adenomatoid malformation (CCAM) is a rare variant of congenital pulmonary cystic disease. It is characterized by cessation of bronchiolar maturation with an over-growth of mesenchymal elements and proliferation of polypoid glandular tissue in the absence of normal alveolar differentiation.
Approximately, 200cases have been reported in the literature in the world and the antenatal diagnosis by ultrasonography has been described in several case reports.
In 80% to 95% of cases, CCAM of the lung is confined to a single lobe and there is no lobe predilection for right and left predominance. The early diagnosis of the lethal macrocystic form of abnormality before a gestational age 25wks allowed the elective termination of pregnancy.
We report one case of this condition where the diagnosis was made antenatally.