즐례 : 베체트병 환자에서 면역억제치료 후 방실전도장애가 호전된 1예 = CASE Reports : A Case of Recovered Atrioventricular Conduction in Behcet Disease after Immunotherapy

국문 초록 (Abstract)

적기에 베체트병의 심혈관침범을 진단하여 면역억제치료를 시작함으로써 방실전도장애가 호전되어 영구형 심장박동기 삽입을 예방할 수 있었던 환자 1예를 보고하는 바이다.

다국어 초록 (Multilingual Abstract)

Atrioventricular conduction disturbance is a rare clinical manifestation of Behcet disease. We describe a case in which a 48-year-old man complaining of dyspnea on exertion presented with complete atrioventricular block with junctional escape rhythm caused by Behcet disease. He also had moderate aortic regurgitation and mitral regurgitation. MRI and PET scan revealed inflammatory changes involving the ventricular septum and the ascending aorta. Recovery of atrioventricular conduction and improvement of valvular regurgitation were achieved with immunotherapy. Timely diagnosis and treatment of cardiac Behcet disease can prevent unnecessary pacemaker implantation. (Korean J Med 2014;86:65-69)

참고문헌 (Reference)

1 Unger P, "Subaortic obstruction and complete atrioventricular block in Behcet's disease" 7 : 250-252, 2006

2 유진석, "Rapidly Progressive Cardiac Manifestation of Behçet’s Disease Involving Conduction System and Aortic Valve" 한국심초음파학회 19 (19): 199-202, 2011

3 Sun RL, "Intra-hisian block associated with unusual etiologies" 10 : 1117-1124, 1987

4 Nojiri C, "Conduction disturbance in Behcet's disease: association with ruptured aneurysm of the sinus of valsalva into the left ventricular cavity" 86 : 636-638, 1984

5 zen Y, "Cardiovascular involvement in Behcet's disease" 29 : 7-12, 2010

6 Lee I, "Cardiac Behcet disease presenting as aortic valvulitis/aortitis or right heart inflammatory mass: a clinicopathologic study of 12 cases" 32 : 390-398, 2008

7 Han JK, "Behcet's disease as a frequently unrecognized cause of aortic regurgitation: suggestive and misleading echocardiography findings" 22 : 1269-1274, 2009

8 Sakane T, "Behcet's disease" 341 : 1284-1291, 1999

9 Lee JS, "A case of ruptured aneurysm of the sinus of valsalva into the left ventricle with complete AV block in Behcet's syndrome" 30 : 107-, 2000

10 Eryol NK, "A case of atrioventricular complete block due to Behcet's disease" 43 : 697-701, 2002