소아에서 발생한 색소성 융기성 피부섬유육종(Bednar 종양) - 1예 보고 - = Pediatric Pigmented Dermatofibrosarcoma Protuberans(Bednar Tumor) - A Case Report -

다국어 초록 (Multilingual Abstract)

A Bednar tumor is a rare neoplasm of intermediate malignant potential that accounts for 1-5%
of all cases of dermatofibrosarcoma protuberans (DFSP). This tumor is considered a pigmented
variant of DFSP, because the clinical and histological findings resemble DFSP. The diagnosis
is commonly made in early to middle adult life except in cases with melanin containing
cells. In the case presented here, the patient was a 3-year-old male who presented with a painless
slow-growing 2.0×1.5×1.0 cm mass on the dorsal aspect of his right hand. Histological
examination of the biopsy specimen revealed typical features of a Bednar tumor, which was
composed of CD34 positive monomorphous spindle shaped cells arranged in a storiform fashion
with moderate mitotic activity (up to 5 per 10 HPF) and scattered pigmented cells with dendritic
processes. We report a rare case of Bednar tumor affecting a pediatric patient and review
the medical literatures.

참고문헌 (Reference)

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