증례 : 혈액종양 ; 불응성 급성전구B림프모세포백혈병 환자에서 발생한 장기종 1예 = Case Reports : Hemato-oncology ; A Case of Pneumatosis Intestinalis in Refractory Acute Precursor B-Cell Lymphoblastic Leukemia-Lymphoma

국문 초록 (Abstract)

장기종은 소화기 장벽내 공기가 축적되는 방사선학적 소견이다. 장기종의 원인은 매우 다양하여 그 원인이 아직 명확하지 않다. 백혈병 환자에서 장기종은 약물치료 및 수술적 치료가 필요한 드문 합병증이다. 대부분의 장기종은 경과 및 예후가 좋은 편이지만 응급수술이 필요한 경우도 있으므로 치료 결정이 어려울 때가 많다. 저자들은 불응성 급성전구B 림프모세포백혈병 환자에서 백혈병의 진행과정으로서 장기종이 발생하여 결국 패혈증으로 사망한 증례를 경험하여 보고하는 바이다.

다국어 초록 (Multilingual Abstract)

Pneumatosis intestinalis (PI) is an imaging phenomenon that represents air in the bowel wall. The cause of PI is variable, although specific etiologic factors remain unknown. It is an infrequent complication in leukemia patients and is associated with several medical and surgical conditions. PI often represents a benign condition, but it can also require surgery. Therefore, the assessment of PI with or without complications can be difficult. Herein, we report on an unusual case of a 63 year-old woman with refractory acute precursor B-cell lymphoblastic leukemia-lymphoma who presented with PI resulting from the leukemic process, and finally expired due to sepsis. (Korean J Med 2011;80:482-485)

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